Using humeral nail for surgical reconstruction of femur in adolescents with osteogenesis imperfecta  

作　　者：Paphon Sa-ngasoongsong Tanyawat Saisongcroh Chanika Angsanuntsukh Patarawan Woratanarat Pornchai Mulpruek 

机构地区：[1]Department of Orthopedics, Faculty of Medicine Ramathibodi Hospital, Mahidol University

出　　处：《World Journal of Orthopedics》2017年第9期735-740,共6页世界骨科杂志（英文版）

摘　　要：Osteogenesis imperfecta(OI) is a rare inherited connective tissue disorder caused by mutation of collagen which results in a wide spectrum of clinical manifestations including long bone fragility fractures and deformities. While the treatment for these fractures was recommended as using intramedullary fixation for minimizing stress concentration, the selection of the best implant in the adolescent OI patients for the surgical reconstruction of femur was still problematic, due to anatomy distortion and implant availability. We are reporting the surgical modification by using a humeral nail for femoral fixation in three adolescent OI patients with favorable outcomes.Osteogenesis imperfecta(OI) is a rare inherited connective tissue disorder caused by mutation of collagen which results in a wide spectrum of clinical manifestations including long bone fragility fractures and deformities. While the treatment for these fractures was recommended as using intramedullary fixation for minimizing stress concentration, the selection of the best implant in the adolescent OI patients for the surgical reconstruction of femur was still problematic, due to anatomy distortion and implant availability. We are reporting the surgical modification by using a humeral nail for femoral fixation in three adolescent OI patients with favorable outcomes.

关 键 词：Osteogenesis imperfecta Adolescent HUMERAL NAIL FEMORAL fracture FEMORAL BOWING DEFORMITY 

分 类 号：R726.8[医药卫生—儿科]