先天性单侧肺静脉闭锁的胸部影像特征  

Thoracic imaging features of congenital unilateral pulmonary vein atresia

作　　者：郭艺帆 何承斌 程建敏[1] 董锋雷 陈博[1] GUO Yifan;HE Chengbin;CHENG Jianmin;DONG Fenglei;CHEN Bo(Department of Radiology,The Second Affiliated Hospital and Yuying Children’s Hospital of Wenzhou Medical University,Wenzhou 325027,China)

机构地区：[1]温州医科大学附属第二医院 育英儿童医院放射科,温州325027

出　　处：《国际医学放射学杂志》2019年第1期94-98,共5页International Journal of Medical Radiology

基　　金：卫生部国家重点临床专科开放课题(20130204);温州市科技计划项目(Y20150287)

摘　　要：目的探讨先天性单侧肺静脉闭锁(UPVA)的胸部影像特征。方法回顾性分析2例UPVA病人的临床表现、影像特征,并复习相关文献。结果胸部平片和CT平扫表现为患侧胸廓小,纵隔向患侧偏移;同侧肺呈弥漫网格、蜂窝状改变;患侧肺门、纵隔区见软组织团块影,其肺侧缘呈现沿支气管血管束的尖状突起。CT血管成像表现为左心房患侧缘光滑,无肺静脉结构;其他处无成形的肺静脉异位引流。结论 UPVA的临床表现缺乏特异性,胸部影像表现具有一定的特征,"纵隔摆动"是本病的一个少见影像征象。Objective To investigate the thoracic imaging features of congenital unilateral pulmonary venous atresia(UPVA).Methods Clinical manifestations and imaging features of two patients with UPVA were analyzed retrospectively,and relevant literatures were reviewed.Results Chest X-ray and CT scan showed a reduced thorax volume of the affected side with mediastinum shift to the affected side,and diffuse reticular opacities or honeycomb in the ipsilateral lung.Furthermore,a low attenuation soft tissue was seen at the affected side pulmonary hilum and mediastinum,and its lateral margin of lung showed a sharp protuberance along the bronchovascular bundle.CT angiography revealed the affected margin of the left atrium was completely smooth without evidence of rudimentary pulmonary veins,and no anomalous pulmonary venous drainage was formed at other sites.Conclusions The clinical manifestations of UPVA are lack of specificity.The chest imaging of UPVA has certain characteristics,and the“pendular movement of mediastinum”is a rare imaging feature of this disease.

关 键 词：肺静脉闭锁 儿童 体层摄影术 X线计算机 

分 类 号：R725.6[医药卫生—儿科] R445[医药卫生—临床医学]