颈位主动脉弓的分型及治疗策略探讨  

Cervical aortic arch: classification and management

作　　者：朱俊明[1] 钟永亮[1] ZHU Jun-ming;ZHONG Yong-liang(Department of Cardiovascular Surgery, Beijing Aortic Disease CentertBeijing Anzhen Hospital, Capital Medical University, Beijing Institute of Heart Lung and Blood Vessel Diseases,Beijing 100029, China)

机构地区：[1]首都医科大学附属北京安贞医院心脏外科北京市大血管疾病诊疗研究中心北京市心肺血管疾病研究所,北京市100029

出　　处：《中国心血管病研究》2019年第9期773-777,共5页Chinese Journal of Cardiovascular Research

基　　金：北京市科委“首都临床特色应用研究”项目(Z17110000107083);国家科技支撑计划项目(2015BAI12B03);心血管疾病精准医学北京实验室(PXM2019_014226_000023).

摘　　要：颈位主动脉弓(cervical aortic arch, CAA)是一种少见的先天性主动脉弓高位畸形,其主动脉弓的位置异常延伸至锁骨上窝或颈部。CAA的发病机制尚不明确,可能与主动脉弓胚胎发育异常和染色体微缺失有关。单纯CAA常无明显临床症状且无需特殊治疗,若合并动脉瘤、主动脉缩窄、血管环压迫症状等则常需手术治疗。由于此类病变解剖复杂、手术难度大,其手术方案应根据其分型、解剖变异及相关合并畸形个体化选择。Cervical aortic arch (CAA) is a rare congenital malformation which the aortic arch locates abnormally high position, extending into the neck or above the level of clavicles. The etiology of CAA remains unknown. It may originate from an embryological malformation of the aortic arch and microdeletion of chromosome. Many patients with isolated CAA are asymptomatic and do not require aggressive intervention, whereas others manifest with aneurysmal dilatation, coarctation of the aorta and vascular ring associated compressive symptoms warrant further assessment and treatment. However, repair of CAA remains an intractable problem due to the complex aortic anatomy. Surgical strategies should be chosen based on types of CAA, anatomic variations and associated anomalies.

关 键 词：颈位主动脉弓 主动脉弓畸形 分型 外科治疗 

分 类 号：R654.2[医药卫生—外科学]