Sturge-Werber综合症的麻醉管理：病例汇报与文献复习  

Anesthesia management of Sturge-Werber syndrome:a case report and review of literatures

作　　者：杜素娟[1] 陈瑞霞[1] 叶西就[1] DU Sujuan;CHEN Ruixia;YE Xijiu(Department of Anesthesia,Sun Yat-Sen Memorial Hospital of Sun Yat-Sen University,Guangzhou510120,China)

机构地区：[1]中山大学孙逸仙纪念医院麻醉科

出　　处：《岭南现代临床外科》2019年第5期600-603,共4页Lingnan Modern Clinics in Surgery

摘　　要：目的探讨Sturge-Werber综合症(SWS)的麻醉管理。方法回顾分析1例Sturge-Werber综合症(Ⅲ型)患儿的麻醉管理,并对相关文献进行复习。结果经过充分的术前评估,了解患者的抗癫痫病史并排除困难气道、眼压增高等风险后,患儿在静吸复合麻醉下顺利完成手术,术后恢复良好。结论困难气道、口腔和上呼吸道血管瘤、中枢神经系统病变、青光眼等是SWS麻醉管理所面临的主要问题。麻醉医师应该充分了解这些问题,并对Sturge-Werber综合症患者进行适当的术前评估从而制定合适的麻醉管理方案。Objective To investigate the anesthesia management of Sturge-Werber syndrome.Methods The anesthesia management of a child with Sturge-Werber syndrome(type Ⅲ)was retrospectively analyzed,and the related literatures were reviewed. Result After sufficient preoperative evaluation,knowing the patient′s history of antiepilepsy and excluding the risks such as difficult airway and high intraocular pressure,the operation was successfully completed under combined intravenous and inhalation anesthesia,and the patient recovered well after operation. Conclusion Difficult airway,oral and upper respiratory angiomata,central nervous system lesions and glaucoma are the main problems in SWS anesthesia management. Anesthesiologists should fully understand these problems and make appropriate preoperative evaluation of SWS patients so as to formulate appropriate anesthesia management plan.

关 键 词：Sturge-Werber综合症 血管瘤 麻醉管理 困难气道 癫痫 

分 类 号：R614[医药卫生—麻醉学]