脑裂畸形的MR影像征象分析(附32例报告)  

Analysis of MR imaging features of schizencephaly

作　　者：曹代荣[1] 李银官[1] 倪希和[1] 林钊[1] 方哲明[1] 郑贤应[1] 

机构地区：[1]福建医科大学附属第一医院CT,MR室,福州350005

出　　处：《放射学实践》2002年第6期468-470,共3页Radiologic Practice

摘　　要：目的 :探讨脑裂畸形的MR影像特征。方法 :回顾性分析 3 2例脑裂畸形的MR表现。结果 :本组 3 2例 ,共42侧裂隙 ,融合型 2 9侧 ,分离型 13侧。其MR影像表现为横贯一侧或双侧大脑半球并衬有灰质的裂隙 ,裂隙外侧端脑表面常见楔形缺损 (3 6/4 2 ) ,其位置大多数在大脑半球凸面中部三分之一 (2 9/4 2 ) ,裂隙内侧端脑室缘呈幕状突起 (19/4 2 )或突向脑室腔的灰质块 (15 /4 2 )。裂隙常与侧裂池相连 (2 6/4 2 ) ,二者位置关系呈直线型、直角型及锐角型三种类型 ,直角型最常见。绝大多数病例侧脑室扩大 (2 9/3 2 ) ,其中 17例对称性扩大 ,12例病灶侧脑室扩大更明显。合并透明隔缺如 2 8例 ,灰质异位 11例 ,多微小脑回 7例。结论 :脑裂畸形的MR影像征象具有特征性 。Objective:To study MR imaging features of schizencephaly.Methods:The MRI appearances of schizencephaly of 32 patients were analyzed retrospectively.Results:In our series,there were 42 clefts,including 29 of closed lip type and 13 of open lip type.Their MR appearances were as followings:gray matter lined full thickness clefts involving one or both cerebral hemispheres;the cerebral surface at the lateral end of the cleft appeared as a wedge shaped defect (36/42);most of them located on the middle 1/3 of cerebral hemispherical convex surface at their lateral end(29/42);diverticulum like protrusion of the lateral ventricle at the medial end of the cleft(19/42) and a gray matter mass projecting to lateral ventricle (15/42) at their medial ends. Most clefts (26/42) communicated with cisterns of lateral fissure in three types:straight line,right angle and acute angle type. In 29 cases with the enlarged lateral ventricles,there were symmetrical (17/29) and asymmetrical (12/29) enlargement. There were 28 cases of accompanying agenesia of septum pellucidum,11 of gray matter ectopia,and 7 of polymicrogyria.Conclusion:For the typical and characteristic MR appearances,MR is con sidered as a gold standard for diagnosing schizencephaly so far.

关 键 词：脑裂畸形 MR影像征象 磁共振成像 诊断 

分 类 号：R445.2[医药卫生—影像医学与核医学]