先天性心脏病并非心脏畸形的研究进展  

Progress on congenital heart disease combined with non-cardiac malformation

作　　者：张伟 屈昕芃 王双兴 张辉[1] 罗毅[1] Zhang Wei;Qu Xinpeng;Wang Shuangxing;Zhang Hui;Luo Yi(Department of Cardiac Surgery,Children′s Hospital,Capital Institute of Pediatrics,Beijing 100020,China)

机构地区：[1]首都儿科研究所附属儿童医院心脏外科,100020

出　　处：《中华实用儿科临床杂志》2019年第24期1917-1920,共4页Chinese Journal of Applied Clinical Pediatrics

摘　　要：先天性心脏病(CHD)居出生缺陷首位。部分CHD患儿合并非心脏畸形,这类患儿围术期病死率和不良事件发生率高于单纯CHD患儿。导致该问题的主要原因之一是CHD合并非心脏畸形的风险评估系统及治疗方案不完善。现通过对这类疾病相关文献的阅读,对其类型及流行病学、诊断和治疗方面的进展进行归纳总结,并对该类疾病的严重程度进行风险分层,对最新手术方案做总结,为CHD合并非心脏畸形患儿的治疗提供参考。Congenital heart disease(CHD)ranks the first in birth defects.Some children with CHD have other non-cardiac malformations,and the perioperative mortality and adverse events are higher in children with CHD.One of the main causes of this problem is that the risk assessment system and treatment plan for CHD with non-cardiac malformations are not perfect.This article summarizes the progress and epidemiology,diagnosis and treatment by reading the literature related to this disease,stratifies the severity of the disease,and summarizes the latest surgical program,and provides evidence for the treatment of patients with CHD and non-cardiac malformations.

关 键 词：先天性心脏病 非心脏畸形 风险分层 治疗 

分 类 号：R72[医药卫生—儿科]