Pulmonary capillary hemangiomatosis or hepatopulmonary syndrome in a patient with calcinosis,Raynaud’s phenomenon,esophageal dysmotility,sclerodactyly and telangiectasia syndrome?  

作　　者：Bijaya Laxmi Shrestha Ying-Kang Jin 

机构地区：[1]Pediatric Department,Guangzhou Medical University,Guangzhou,Guangdong 510623,China [2]Pediatric Pulmonary Department,Guangzhou Women and Children’s Medical Center,Guangzhou Medical University,Guangzhou,Guangdong 510623,China

出　　处：《Chinese Medical Journal》2020年第2期243-244,共2页中华医学杂志（英文版）

摘　　要：To the Editor:We were interested in the article,which reported a woman with calcinosis,Raynaud’s phenomenon,esophageal dysmotility,sclerodactyly and telangiectasia(CREST)syndrome who developed progressive dyspnea on exertion and was later diagnosed with pulmonary capillary hemangiomatosis(PCH)that was confirmed by an open lung biopsy.[1]We would like to remark that the diagnosis of PCH is inconclusive from just history,treatment,and histological changes.This case also does not specify a clear connection between PCH and CREST syndrome;therefore,we believe we need to explore another possible disease association.

关 键 词：ESOPHAGEAL MOTILITY diagnosis 

分 类 号：R725.6[医药卫生—儿科]