高场强MRI在婴幼儿期Sturge-Weber综合征诊断中的应用价值  

The Value of High Field MRI in the Diagnosis of Sturge-Weber Syndrome in Infants

作　　者：于啸 汪秀玲 张欣贤 辛涛 李钱程 郭迪 YU Xiao;WANG Xiu-ling;ZHANG Xin-xian(Department of Radiology,Xuzhou Children's Hospital,Xuzhou Medical University,Xuzhou 221000,Jiangsu Province,China)

机构地区：[1]徐州医科大学附属徐州儿童医院影像科,江苏徐州221000 [2]徐州医科大学附属医院影像科,江苏徐州221000

出　　处：《中国CT和MRI杂志》2020年第9期20-23,共4页Chinese Journal of CT and MRI

摘　　要：目的探讨婴幼儿期Sturge-Weber综合征MRI影像特征及其临床诊断价值。方法搜集PACS系统中10例Sturge-Weber综合征患儿的MRI图像进行回顾性分析,10例患儿均行MRI平扫及增强检查,3例行SWAN序列扫描。结果本组患儿均存在面部三叉神经分布区的血管瘤,MRI扫描显示9例病变累及单侧大脑半球,1例累及双侧大脑半球,6例见患侧侧脑室脉络丛扩大,5例伴有局部脑萎缩,5例可见病变区脑白质T2WI信号明显减低。10例均行增强SE T1WI及增强T2-FLAIR序列扫描,患侧脑回表面软脑膜均有强化,其中软脑膜血管瘤在增强T2-FLAIR序列显示7例,在增强SE T1WI序列显示3例。磁敏感加权T2*加权血管成像(SWAN)检查可见多发扩张增粗深静脉影。结论婴幼儿脑颜面血管瘤MRI表现具有特征性,尤其是增强T2 FLAIR序列发现软脑膜血管瘤强化可作为诊断本病的最直接依据,有助于临床尽早治疗、改善预后。Objective To investigate the MRI imgaging features and clinical diagnostic value of Sturge-Weber syndrome(SWS) in infants.Methods The MRI features of 10 children with Sturge-Weber syndrome in PACS were retrospectively analyzed.All had plain MRI and enhanced examination,3 patients underwent SWAN sequence.Results All the children had facial hemangioma in the trigeminal region,MRI scans showed that 9 patients involved unilateral cerebral spheres,1 patient had bilateral cerebral sphere involved,6 cases were with ipsilateral enlargement of choroids plexus.5 patients were with local brain atrophy,The white matter T2WI signal was significantly reduced in 5 cases.All the patients with enhanced SE T1WI and enhanced T2 FLAIR sequence scans showed that ipsilateral leptomeningeal was enhanced.Among them,leptomeningeal hemangioma was revealed in 7 cases with enhanced T2 FLAIR sequence and 3 cases with enhanced SE T1WI sequence.SWAN sequence examination showed multiple expansion and thickening of deep veins.Conclusion The MRI features of SWS in infants are characteristic,especially the enhancement of T2 FLAIR sequence with the enhancement of leptomeningeal hemangioma can be used as the most direct basis for the diagnosis,which is helpful for early treatment and prognosis.

关 键 词：STURGE-WEBER综合征 婴幼儿 磁共振成像 增强扫描 

分 类 号：R445.2[医药卫生—影像医学与核医学] R5[医药卫生—诊断学]