肥厚型心肌病与左室肥厚性疾病的影像学鉴别进展  

Progress on differentiation hypertrophic cardiomyopathy from other causes of left ventricular hypertrophy

作　　者：李烨 黄璇 张乔柔 姜萌[1] LI Ye;HUANG Xuan;ZHANG Qiaorou;JIANG Meng(Department of Cardiology,Shanghai Jiao Tong University School of Medicine,Shanghai,200127,China)

机构地区：[1]上海交通大学医学院附属仁济医院心内科,上海200127

出　　处：《临床心血管病杂志》2020年第8期696-700,共5页Journal of Clinical Cardiology

基　　金：国家自然科学基金(No:81971570);上海申康医院发展中心促进市级医院临床技能与临床创新能力三年行动计划项目(No:16CR3020A);浦东新区联合攻关项目(No:PW2018D-03);医工交叉基金资助项目(No:YG2019ZDA13)。

摘　　要：肥厚型心肌病(HCM)是最常见的遗传性心肌病,以心室壁过度增厚、晕厥、早发猝死为主要表现。左室肥厚是HCM的病变特征,然而现有诊断标准不能将其与心脏负荷过重引起的左室肥厚性疾病准确区分,如运动员心脏、高血压性心脏病(HHD)、心肌淀粉样变性(CA)等。本文主要对HCM与左室肥厚相关疾病的影像学鉴别进展作一综述。Hypertrophic cardiomyopathy(HCM)is the most common genetic cardiomyopathy and is a disease characterized by left ventricle wall thickness,syncope and early sudden death.Excessive left ventricle wall thickness is the pathological feature of HCM.However,differentiating HCM from other causes of left ventricular hypertrophy,such as athlete’s heart,hypertensive heart disease(HHD),cardiac amyloidosis(CA)encounters diagnostic challenges.This article reviews the research progress of radiology in this respect,providing radiological support for clinical differential diagnosis.

关 键 词：肥厚型心肌病 运动员心脏 高血压性心脏病 心肌淀粉样变性 

分 类 号：R542.2[医药卫生—心血管疾病]