Benign symmetric lipomatosis (Madelung’s disease) with concomitant incarcerated femoral hernia: A case report  

作　　者：Bo Li Zheng-Xing Rang Jia-Cong Weng Guo-Zuo Xiong Xian-Peng Dai 

机构地区：[1]Department of Vascular and Hernia Surgery,The Second Affiliated Hospital of Nanhua University,Hengyang 421001,Hunan Province,China

出　　处：《World Journal of Clinical Cases》2020年第21期5474-5479,共6页世界临床病例杂志

摘　　要：BACKGROUND Benign symmetric lipomatosis(BSL)was first described by Brodie in 1846 and defined as Madelung’s disease by Madelung in 1888.At present,about 400 cases have been reported worldwide.Across these cases,surgical resection remains the recommended treatment.Here we report a case of neck BSL with concomitant thick fatty deposit in the inguinal region,which concealed the signs of a right incarcerated femoral hernia.CASE SUMMARY A 69-year-old male patient was admitted to our hospital with“abdominal pain,abdominal distension,nausea-vomiting and difficult defecation for half a month”.Moreover,he had a mass in the right inguinal region for more than 10 years.An egg-sized neck mass also developed 15 years ago and had developed into a full neck enlargement 1 year later.In addition,the patient had a history of heavy alcohol consumption for more than 40 years.With the aid of computerized tomography scan,the patient was diagnosed with BSL and a low intestinal mechanical obstruction caused by a right inguinal incarcerated hernia.Under general anesthesia,right inguinal incarcerated femoral hernia loosening and tension-free hernia repair was performed.However,this patient did not receive BSL resection.After a 1-year follow-up,no recurrence of the right inguinal femoral hernia was found.Moreover,no increase in fat accumulation was found in the neck or other areas.CONCLUSION Secretive intraperitoneal fat increase may be difficult to detect,but a conservative treatment strategy can be adopted as long as it does not significantly affect the quality-of-life.

关 键 词：Benign symmetric lipomatosis Madelung’s disease Neck Inguinal region Inguinal incarcerated hernia Case report 

分 类 号：R589.2[医药卫生—内分泌]