川崎病休克综合征的诊治进展  

Progress in diagnosis and treatment of Kawasaki disease shock syndrome

作　　者：陈夜 肖东琼[1] CHEN Ye;XIAO Dong-qiong(Department of Emergency Medicine,West China Second University Hospital,Sichuan University,Key Laboratory of Birth Defects and Related Diseases of Women and Children of the Ministry of Education,Sichuan Province,Chengdu610041,China)

机构地区：[1]四川大学华西第二医院急诊医学科,出生缺陷与相关妇儿疾病教育部重点实验室,四川成都610041

出　　处：《中国当代医药》2021年第7期20-23,共4页China Modern Medicine

基　　金：国家自然科学基金资助项目(82001593)。

摘　　要：川崎病(KD)是一种以发热为主要表现的儿童常见血管炎。川崎病休克综合征(KDSS)是KD的一种罕见表现,其特点是收缩压持续低于同龄儿童正常收缩压低值20%及以上,或伴有组织灌注不良的一种临床征象。由于其早期症状不典型,临床上常常与感染性休克混淆,从而影响患儿的诊治,因此早期识别该病对于儿科临床医生尤为重要。本文从KDSS的发病机制、临床表现、实验室指标、治疗和预后等方面对其进行归纳总结,以便尽早治疗,进而改善患儿的预后。Kawasaki disease(KD)is a common vasculitis in children with fever as the main manifestation.Kawasaki disease shock syndrome(KDSS)is a rare form of KD,characterized by sustained systolic blood pressure lower than 20%or more of normal low systolic blood pressure in children of the same age,or accompanied by a clinical sign of poor tissue perfusion.Because its early symptoms are not typical,it is often confused with septic shock in clinical practice,which affects the diagnosis and treatment of children.Therefore,early recognition of the disease is particularly important for pediatric clinicians.This article summarizes KDSS from its pathogenesis,clinical manifestations,laboratory indicators,treatment and prognosis,so as to facilitate early treatment and improve the prognosis of children.

关 键 词：川崎病 川崎病休克综合征 诊断 治疗 

分 类 号：R725.9[医药卫生—儿科]