影像学上诊断为蜗神经未发育患者听力损失的特征分析  

The analysis of the characteristics of hearing loss in patients with cochlear nerve aphasia identified by MRI

作　　者：梅玲[1] 陈向平[1] 杨军[1] MEI Ling;CHEN Xiangping;YANG Jun(Hearing and Vertigo Center,Xinhua Hospital.Medical School of Shanghai Jiaotong University,Shanghai,200092,China)

机构地区：[1]上海交通大学医学院附属新华医院听力障碍和眩晕诊治中心,上海200092

出　　处：《临床耳鼻咽喉头颈外科杂志》2021年第1期14-16,共3页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

摘　　要：目的:探讨蜗神经未发育(CNA)患者听力损失的特征,为临床此类患者的诊断和治疗提供依据。方法:回顾性分析51例CNA患者的听力学结果、颞骨HRCT和内听道MRI检查结果,分析患者听力损失的特征。结果:77.19%的患耳呈极重度听力损失,7.02%的患耳呈中度听力损失;CNA患耳的残余听力集中分布于低中频;伴蜗神经孔闭锁的CNA的患耳可表现为中度听力损失。结论:CNA患者仍有残余听力的可能性。中度听力损失的患者不排除CNA的可能。内听道MRI、颞骨薄层HRCT扫描和听力学评估的"三维一体"的综合评估体系更有助于对CNA疾病的诊断。Objective: To explore the characteristics of hearing loss in patients with cochlear nerve aphasia(CNA) and to provide evidences for diagnosis and treatment of cochlear nerve aphasia. Methods: A retrospective study was performed. A total of 51 cases were included in the study. The data of hearing test, inner auditory canal MRI and temporal HRCT were analyzed. Results: 77.19% of the affected ears had extremely severe hearing loss, and 7.02% of the affected ears had moderate hearing loss. The residual hearing was concentrated in low-medium frequency. A CNA ear with bone cochlear nerve canal atresia can exhibited moderate hearing loss.Conclusion: The patient with CNA may still present residual hearing function. CNA could not be excluded in patients with moderate hearing loss. The "three-dimensional integration" comprehensive evaluation system, which includesinternal auditory canal MRI, temporal thin-layer CT scan and audiology evaluation, could be helpful to the diagnosis of cochlear nerveaphasia.

关 键 词：蜗神经 发育不良 听力损失 

分 类 号：R764.43[医药卫生—耳鼻咽喉科]