Ⅰ型糖原累积症患儿饮食管理的研究进展  

Research progress of diet management in children with glycogen storage disease typeⅠ

作　　者：袁琳 邱正庆[2] 李融融[3] 孙静[2] 李杨[1] Yuan Lin;Qiu Zhengqing;Li Rongrong;Sun Jing;Li Yang(School of Nursing,Peking Union Medical College,Beijing 100144,China;Department of Pediatrics,Peking Union Medical College Hospital,Beijing 100730,China;Nutrition Department,Peking Union Medical College Hospital,Beijing 100730,China)

机构地区：[1]北京协和医学院护理学院,100144 [2]北京协和医院儿科,100730 [3]北京协和医院营养科,100730

出　　处：《中华现代护理杂志》2021年第11期1522-1525,共4页Chinese Journal of Modern Nursing

摘　　要：对于Ⅰ型糖原累积症患儿,饮食管理能够最优化地维持机体葡萄糖内环境的稳定,纠正或改善代谢紊乱,并保持最佳营养状态,促进患儿自身生长和发育。本文对Ⅰ型糖原累积症患儿饮食管理的研究进展进行综述,重点探讨Ⅰ型糖原累积症患儿饮食管理现状和现存问题,以期为我国开展和实践Ⅰ型糖原累积症患儿饮食管理提供借鉴和参考。For children with glycogen storage disease typeⅠ,diet management can optimally maintain the stability of the body's glucose internal environment,correct or improve metabolic disorders,and maintain the best nutritional status,and promote the growth and development of children.This article reviews the research progress of diet management in children with glycogen storage disease typeⅠ,focusing on the current status and existing problems of diet management in children with glycogen storage disease typeⅠ,so as to provide a reference for developing and practicing the diet management for children with glycogen storage disease typeⅠin China.

关 键 词：综述 儿童 Ⅰ型糖原累积症 饮食管理 

分 类 号：R473.72[医药卫生—护理学]