右室双出口外科治疗进展——双心室矫治是首选  

Frontiers in surgical management of double outlet right ventricle:biventricular repair is a preferred strategy.

作　　者：李守军[1] Li Shoujun(Department of Cardiovascular Surgery,Fuwai Hospital,National Center for Cardiovascular Diseases,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100037,China.)

机构地区：[1]中国医学科学院,北京协和医学院,国家心血管病中心,心血管疾病国家重点实验室,阜外心血管病医院小儿心脏外科中心,北京市100037

出　　处：《临床小儿外科杂志》2021年第6期501-505,共5页Journal of Clinical Pediatric Surgery

基　　金：十三五国家重点研发计划(编号:2017YFC1308100)。

摘　　要：右室双出口(double outlet right ventricle,DORV)是病理解剖复杂多样的一类先天性心脏病,其外科手术方式多样,主要以双心室解剖矫治及单心室姑息治疗为主。不同病理解剖类型的DORV手术复杂程度不同,随着技术的进步和规范,对于左右心室发育均衡、房室瓣功能尚佳的DORV患者,双心室矫治是手术治疗的优选策略。Double-outlet right ventricle(DORV)is a complex congenital heart disease encompassing various common and rare subtypes.Two major surgical approaches of biventricular repair and single ventricular palliation are routinely applied.Surgery remains rather complicated in some subtypes of DORV.With ongoing development and standardization of surgical managements and techniques,biventricular repair has become a preferred option for DORV.

关 键 词：右室双出口/外科学 右室双出口/分类 心脏缺损 先天性/外科学 心脏缺损 先天性/诊断 临床方案 治疗结果 

分 类 号：R541.1[医药卫生—心血管疾病] R493.28[医药卫生—内科学]