罕见病颅内磷酸盐尿性间叶性肿瘤疾病和编码的探讨  

Study on the disease coding of rare intracranial phosphaturia mesenchymal tumor

作　　者：汪满仙[1] 潘邦盛 谢湘媚[1] 雷芳 饶兆伟 WANG Manxian;PAN Bangsheng;XIE Xiangmei;LEI Fang;RAO Zhaowei(Foshan Hospital of traditional Chinese Medicine,Foshan 528000,China;不详)

机构地区：[1]佛山市中医院,广东佛山528000

出　　处：《现代医院》2021年第6期925-926,929,共3页Modern Hospitals

摘　　要：目的学习探讨罕见颅内原发性磷酸盐尿性间叶性肿瘤(Phosphaturic mesenchymal tumor,PMT)疾病的病理特点,通过对临床和病理相关知识的学习,以提高对罕见病的编码水平。方法分析一例罕见颅内磷酸盐尿性间叶性肿瘤的发病机理、病理和临床表现,按照ICD-10的分类原则,探寻正确的编码方法。结果颅内磷酸盐尿性间叶性肿瘤(PMT)多发于骨及软组织,四肢是其好发部位,颅内和神经系统非常罕见,由于肿瘤镜下形态易于与其他软组织肿瘤相混淆,且影像学上与硬脑膜瘤十分相似,容易误诊为脑膜瘤。结论通过学习PMT的相关临床和病理知识,主动与临床和病理医生沟通,本例颅内磷酸盐尿性间叶瘤最终确诊为混合性间叶瘤M89901/1,D48.102。通过对罕见病相关知识的学习,提高了编码的准确率。Objective To Study and explore the pathological characteristics of rare intracranial primary phosphateuria mesenchymal tumor(PMT)diseases,and improve the coding level of rare diseases through the study of clinical and pathological knowledge.Methods Analyze the pathogenesis,pathology and clinical manifestations of a rare case of intracranial phosphateuria mesenchymal tumor,and search for the correct coding method according to the classification principle of ICD-10.Results Intracranial phosphateuria mesenchymal tumors(PMT)mostly occur in bones and soft tissues.The extremities are the most common sites.The intracranial and nervous system are very rare.Because the tumor’s microscopic morphology is easy to be confused with other soft tissue tumors,and imaging It is very similar to duramatoma,and it is easy to be misdiagnosed as meningiomas.Conclusion Through learning the relevant clinical and pathological knowledge of PMT,and actively communicating with clinicians and pathologists,this case of intracranial phosphateuria mesenchymal tumor was finally diagnosed as mixed mesenchymal tumor M89901/1,D48.102.Through the learning of rare diseases related knowledge,the accuracy of coding is improved.

关 键 词：磷酸盐尿性间叶性肿瘤 病理 疾病分类ICD-10 

分 类 号：R197.323.1[医药卫生—卫生事业管理]