混合型完全性肺静脉异位引流的解剖特征及治疗进展  

Recent advances in anatomy and treatment of mixed-type total anomalous pulmonary venous connection

作　　者：曾国炜(综述) 武开宏(审校)[1] Zeng Guowei;Wu Kaihong(Department of Cardiothoracic Surgery,Children's Hospital of Nanjing Medical University,Nanjing 210008,China)

机构地区：[1]南京医科大学附属儿童医院心胸外科,江苏省南京市210008

出　　处：《临床小儿外科杂志》2021年第9期881-885,共5页Journal of Clinical Pediatric Surgery

基　　金：江苏省卫生计生委医学科技发展基金(编号:ZDRCA2016073);南京市中青年拔尖人才项目(编号:NJBJ2020001)。

摘　　要：完全性肺静脉异位引流(total anomalous pulmonary venous connection,TAPVC)作为一种少见的先天性心脏病,是儿科领域少数需行急诊手术的心脏疾病之一,而混合型TAPVC占所有TAPVC的5%~10%。由于混合型TAPVC解剖变异类型众多且没有确切的手术方式,导致其病死率一直较高,因此明确患者的解剖结构对手术方式的选择、减少术后并发症及改善患者的预后至关重要。本文旨在总结混合型TAPVC解剖及治疗领域的研究成果,重点阐述新解剖分型与手术方法选择、术后肺静脉梗阻发生之间的关系,以期为混合型TAPVC的临床治疗提供参考。As a rare congenital heart disease,total anomalous pulmonary venous connection(TAPVC)is one of few pediatric heart diseases requiring emergency surgery.Mixed type accounts for about 5%~10%.Because of numerous anatomic variants of mixed TAPVC,no definite operative mode results in its persistent high mortality.Elucidating distinct anatomical structures remains vital for selecting surgical approaches,reducing postoperative complications and optimizing the prognosis.This review summarized the research findings of anatomy and treatment of mixed TAPVC,focusing upon selecting new anatomical classifications and surgical modes and the postoperative occurrences of pulmonary vein obstruction to provide references for clinical management of mixed TAPVC.

关 键 词：心脏病/先天性 完全性肺静脉异位引流/外科学 治疗 心脏/解剖学和组织学 

分 类 号：R725.415[医药卫生—儿科] R541[医药卫生—临床医学]