肺动脉闭锁伴室间隔缺损的外科手术策略进展  

Progress in surgical strategies of pulmonary atresia with ventricular septal defect

作　　者：宋治莹 郑景浩[1] SONG Zhi-ying;ZHENG Jing-hao(Department of Cardiothoracic Surgery,Shanghai Children's Medical Center,Shanghai Jiao Tong University School of Medicine,Shanghai 200127,China)

机构地区：[1]上海交通大学医学院附属上海儿童医学中心心胸外科,上海200127

出　　处：《上海交通大学学报（医学版）》2021年第10期1389-1393,共5页Journal of Shanghai Jiao tong University:Medical Science

基　　金：上海市科学技术委员会资助项目(19411963700)。

摘　　要：肺动脉闭锁伴室间隔缺损是最为常见的复杂右心畸形之一。大型主肺侧支动脉的存在及肺血管发育个体差异化明显,使得该畸形的解剖分型及外科手术方式多样,治疗效果不甚理想。目前,国内外尚缺乏针对单源化手术和分期手术等治疗策略的统一标准和流程。该文就肺动脉闭锁伴室间隔缺损的外科诊治及手术策略进展进行综述。Pulmonary atresia with ventricular septal defect is one of the most common complex right heart malformations.The existence of major aortopulmonary collateral arteries and the individual differences in pulmonary vascular development make the anatomical classification and surgical methods of this disease variable,and the treatment effect is not ideal.At present,there is still a lack of unified standards and procedures for treatment strategies such as unifocalization and staged surgery at home and abroad.This article reviews the progress of surgical diagnosis and treatment and surgical strategy of pulmonary atresia with ventricular septal defect.

关 键 词：肺动脉闭锁 室间隔缺损 大型主肺侧支动脉 手术策略 

分 类 号：R726.1[医药卫生—儿科]