白塞综合征诊疗规范  

Recommendations for the diagnosis and treatment of Behçet′s syndrome in China

作　　者：郑文洁 张娜[2] 朱小春[3] 池淑红[4] 张文 魏蔚[2] 赵岩 董怡 Zheng Wenjie;Zhang Na;Zhu Xiaochun;Chi Shuhong;Zhang Wen;Wei Wei;Zhao Yan;Dong Yi(Department of Rheumatology and Clinical Immunology,Peking Union Medical College,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences,National Clinical Research Center for Dermatologic and Immunologic Diseases,Ministry of Science&Technology,State Key Laboratory of Complex Severe and Rare Diseases,Key Laboratory of Rheumatology and Clinical Immunology,Ministry of Education,Beijing 100730,China;Department of Rheumatology and Clinical Immunology,Tianjin Medical University General Hospital,Tianjin 300052,China;Department of Rheumatology,the First Affiliated Hospital of Wenzhou Medical University,Wenzhou 325000,China;Department of Rheumatology,General Hospital of Ningxia Medical University,Yinchuan 750004,China)

机构地区：[1]中国医学科学院,北京协和医学院,北京协和医院风湿免疫科,国家皮肤与免疫疾病临床医学研究中心,疑难重症及罕见病国家重点实验室,风湿免疫病学教育部重点实验室,100730 [2]天津医科大学总医院风湿免疫科,300052 [3]温州医科大学第一附属医院风湿免疫科,325000 [4]宁夏医科大学附属医院风湿免疫科,银川750004

出　　处：《中华内科杂志》2021年第10期860-867,共8页Chinese Journal of Internal Medicine

摘　　要：白塞综合征是一种病因未明的全身慢性血管炎症性疾病,临床表现多样,且缺乏特异性实验室指标,临床误诊和漏诊率较高。中华医学会风湿病学分会在借鉴国内外诊治经验和指南的基础上,制定了本诊疗规范,旨在规范白塞综合征诊断及各系统受累的治疗策略,减少误诊漏诊及严重不良事件的发生,改善患者预后。Behçet′s syndrome(BS)is classified among variable vessel vasculitis with unknown etiology and extensively heterogeneous clinical features.It is easily missed or misdiagnosed due to the lack of a specific laboratory diagnosis index.Based on the evidence and guidelines from China and other countries,the Chinese Rheumatology Association developed the standardization of diagnosis and treatment of BS.The purposes are:(1)To standardize the detection and interpretation of key indicators for BS;(2)To standardize rational management for BS patients with topical and systemic organ involvement to reduce complications and improve outcomes.

关 键 词：贝赫切特综合征 诊断 治疗 预后 

分 类 号：R597.9[医药卫生—内科学]