儿童中枢神经系统非典型畸胎样/横纹肌样瘤的影像表现  

Image features of atypical teratoid/rhabdoid tumor of central nervous system in children

作　　者：李艳华[1] 彭芸[1] 白洁 温洋[1] 张宁宁[1] 程华[1] 刘玥[1] LI Yanhua;PENG Yun;BAI Jie;WEN Yang;ZHANG Ningning;CHENG Hua;LIU Yue(Imaging Center,Beijing Children's Hospital,Capital Medical University,National Center for Children's Health,Beijing 100045,China)

机构地区：[1]首都医科大学附属北京儿童医院,国家儿童医学中心,北京100045

出　　处：《磁共振成像》2021年第10期49-52,56,共5页Chinese Journal of Magnetic Resonance Imaging

摘　　要：目的探讨儿童中枢神经系统非典型畸胎样/横纹肌样瘤(atypical teratoid/rhabdoid tumor,AT/RT)的影像表现,提高对该肿瘤的诊断水平。材料与方法回顾性分析2017年6月~2021年1月经病理证实的9例(男4例,女5例)AT/RT患儿的临床和影像资料。结果患儿中位年龄19个月,年龄范围5个月~39个月,原发灶位于幕下5例,幕上1例,幕上、幕下同时受累3例。瘤体最大径49.9±18.3 mm,伴有偏心囊变7例,瘤体出血6例,脑转移3例,脑、脊髓同时转移1例;瘤体实性成分在CT上以等或高密度为主,MRI T2WI信号混杂,DWI上瘤体实性成分呈高信号,ADC图为低信号,瘤体强化模式多样。结论小儿中枢神经系统AT/RT具有一定特征性影像表现,有助于诊断。Objective: To investigate the imaging findings of central nervous system(CNS) atypical teratoid/rhabdoid tumor(AT/RT)in children and to improve the diagnostic level of AT/RT. Materials and Methods: The clinical and image data of 9 children with AT/RT were analyzed retrospectively. Results: The median age of patients was 19 months, 5 cases were infratentorial, 1 case was supratentorial,3 cases involved both supratentorial and infratentorial. The maximum diameter of the tumor was 49.9±18.3 mm, 7 cases with peripheral tumor cysts and 6 cases with intratumoral hemorrhage, 3 cases with brain metastasis, 1 with both brain and spinal cord metastasis. The solid components of the tumor were mainly iso-or high-density on CT, MRI showed mixed intensity on T2 WI and high intensity on DWI with low ADC value, the tumor showed various enhancement modes. Conclusion: CNS AT/RT of children have some relatively specific imaging findings, which is helpful for diagnosis.

关 键 词：非典型畸胎样/横纹肌样瘤 中枢神经系统 影像诊断 磁共振成像 表观扩散系数 

分 类 号：R445.2[医药卫生—影像医学与核医学] R739.4[医药卫生—诊断学]