无顶冠状静脉窦综合征临床及影像学研究进展  

Advances in clinical research and imaging of unroofed coronary sinus syndrome

作　　者：张慧慧 矫妮[1] 李静[1] 李颖[1] 丁明岩[1] 朱芳[1] ZHANG Hui-hui;JIAO Ni;LI Jing;LI Ying;DING Ming-yan;ZHU Fang(Department of Cardiovascular Function,People’s Hospital of China Medical University,the People’s Hospital of Liaoning Province,Shenyang,Liaoning 110001,China)

机构地区：[1]辽宁省人民医院暨中国医科大学人民医院心功能科,辽宁沈阳110001

出　　处：《中华实用诊断与治疗杂志》2021年第10期1074-1076,共3页Journal of Chinese Practical Diagnosis and Therapy

基　　金：辽宁省科学技术计划项目(2020JH4/10100040)。

摘　　要：无顶冠状静脉窦综合征是一种罕见的先天性心脏畸形,是冠状静脉窦和左心房之间管壁部分或完全缺失,在先天性心脏病中的发病率为0.2%~0.3%。无顶冠状静脉窦常合并一些其他畸形,75%的无顶冠状静脉窦患者合并永存左上腔静脉。临床症状可表现为心慌、胸闷、呼吸困难、体位性或暂时性发绀、缺氧或完全无症状。因患者通常缺乏特异性临床表现,临床易漏诊、误诊。本文就无顶冠状静脉窦综合征的胚胎发育、临床症状、影像学诊断方法及治疗的研究进展作一综述。Unroofed coronary sinus syndrome is a rare type of congenital heart malformation, with an incidence of 0.2% to 0.3% in congenital heart diseases. There is a partial or complete absence of coronary sinus roof between the vein and left atrium. Unroofed coronary sinus syndrome is usually complicated with other anomalies, and 75% of the patients with unroofed coronary sinus syndrome have persistent left superior vena cava. The clinical symptoms of unroofed coronary sinus syndrome include palpitation, chest distress, breathing difficulties, postural or temporary cyanosis, hypoxia, or none at all. Because of lacking specific clinical manifestations, it is not valued by clinicians. This paper reviews the research progress of the development of embryonic development, clinical symptoms, imaging diagnostic methods and treatment of insecure coronary sinus syndrome.

关 键 词：无顶冠状静脉窦综合征 永存左上腔静脉 先天性心脏畸形 

分 类 号：R541.1[医药卫生—心血管疾病]