青年心肌致密化不全合并心力衰竭1例并文献复习  

Youth noncompaction of ventricular myocardium complicating heart failure:a case report and literature review

作　　者：韩蕊 梅迎晨 马旃[1] 韩昊[1] 王继红[1] HAN Rui;MEI Yingchen;MA Zhan;HAN Hao;WANG Jihong(Department of Cardiology,Beijing Jishuitan Hospital,Beijing 100035,China)

机构地区：[1]北京积水潭医院心内科,100035

出　　处：《重庆医学》2021年第21期3647-3651,共5页Chongqing medicine

基　　金：国家自然科学基金青年科学基金项目(81700330);北京市优秀人才青年个人项目(2016000021469G176)。

摘　　要：目的系统回顾心肌致密化不全(NVM)的疾病特点及诊治要点,并总结该病的治疗经验。方法回顾性分析2020年4月2—18日及9月2—7日该院心内科入院收治的1例NVM合并心律失常、心力衰竭及血栓栓塞等多种并发症的青年患者的诊治经过,并系统随访11个月,观察患者预后。结果积极控制并纠正心律失常后患者心脏结构及功能呈现可逆性改善。结论NVM是临床较为罕见的先天性心肌病。其临床表现多样而不典型,可出现包括心律失常、心力衰竭、血栓栓塞等多种不良事件,甚至可出现心源性猝死等恶性后果。临床医师需加强对该病的认识,为及时确诊并合理治疗提供可能。Objective To systematically review the characteristics,diagnosis and treatment of noncompaction of the ventricular myocardium(NVM),and to summary its treatment experience.Methods The diagnosis and treatment process in 1 case of NVM complicating arrhythmia,heart failure and thromboembolism in the cardiology department of this hospital April 2-18 and September 2-7,2020 was retrospectively analyzed.The case was followed up for 11 months and the prognosis was observed.Results The cardiac structure and function of the patients showed the reversible improvement after active control and correction of arrhythmia.Conclusion NVM is a rare congenital cardiomyopathy.Its clinical manifestations are diverse and atypical,including arrhythmia,heart failure,thromboembolism and other adverse events,as well as even malignant outcomes such as sudden cardiac death.It is necessary to strengthen the understanding of the disease in order to provide the possibility of timely diagnosis and reasonable treatment to the patients with NVM.

关 键 词：心肌病 心肌致密化不全 心力衰竭 心房颤动 

分 类 号：R542.2[医药卫生—心血管疾病]