结蛋白肌病相关的心力衰竭和心律失常一例  

A case of heart failure and arrhythmia associated with desmin myopathy

作　　者：刘元 李博[1] 王琳[1] 林旭 刘栩含 张尉华[1] Liu Yuan;Li Bo;Wang Lin;Lin Xu;Liu Xuhan;Zhang Weihua(Department of Cardiology,The First Hospital of Jilin University,Changchun 130021,China)

机构地区：[1]吉林大学第一医院心血管内科,长春130021

出　　处：《中华心力衰竭和心肌病杂志（中英文）》2021年第2期114-117,共4页Chinese Journal of Heart Failure and Cardiomyopathy

基　　金：国家重点研发计划项目(2016YFC1301002)。

摘　　要：结蛋白肌病主要表现为下肢对称性远端肌无力,部分病例累及心肌和心脏传导系统。本文报道1例少见的结蛋白肌病病例,双侧心室心肌受累导致心力衰竭以及传导系统受累导致束支传导阻滞。Desmin myopathy is mainly characterized by symmetrical distal muscle weakness of the lower extremity,and myocardium and cardiac conduction system may involve in some cases.This paper reports a rare case of bilateral ventricular myocardial involvement leading to heart failure and cardiac conduction system involvement resulting in bundle branch block.

关 键 词：结蛋白肌病 心力衰竭 心脏传导系统 

分 类 号：R541.6[医药卫生—心血管疾病] R541.7[医药卫生—内科学]