以弥漫性肺泡出血为主要表现的多发性肌炎伴多脏器功能障碍综合征1例  被引量:1

Polymyositis presenting as diffuse alveolar hemorrhage and with multiple organ dysfunction syndrome: a case report

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作  者:关云艳[1] 吴锡平[1] 王倩[1] 王亮[1] 孙月雯[1] 沈丽娟[1] GUAN Yunyan;WU Xiping;WANG Qian

机构地区:[1]无锡市中医医院重症医学科,江苏无锡214071

出  处:《临床急诊杂志》2022年第1期72-75,共4页Journal of Clinical Emergency

摘  要:弥漫性肺泡出血是由肺泡毛细血管炎症所导致的持续的肺出血,病因多为毒物吸入、感染、凝血功能异常及自身免疫性疾病,在自身免疫性疾病中又常见于系统性红斑狼疮、抗中性粒细胞胞浆抗体(ANCA)相关性血管炎、Good-Pasture综合征等^ [1],而在多发性肌炎患者中并发肺泡出血者很罕见。现报道我科于2020年成功救治的1例以弥漫性肺泡出血为主要表现的多发性肌炎同时伴多脏器功能障碍患者的救治经过,并进行相关文献复习。Polymyositis often presents a chronic course, and it is not uncommon for interstitial lung disease to be the first manifestation. However, it is very rare for patients with diffuse alveolar hemorrhage and multiple organ dysfunction after admission. The above complications can significantly increase the risk of death. This paper reports the treatment of a case of polymyositis with multiple organ dysfunction syndrome and diffuse alveolar hemorrhage as the main manifestation in our department in 2020, and summarizes the experience and reviews the relevant literatures.

关 键 词:多发性肌炎 弥漫性肺泡出血 多脏器功能障碍综合征 

分 类 号:R593.26[医药卫生—内科学]

 

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