Staging surgery for intraventricular bilateral giant Rosai–Dorfman disease in children  

作　　者：Jiyin Zhang Dapeng Li Ran Cheng Nan Zhang Xin Ni Ming Ge 

机构地区：[1]Department of Otolaryngology,Head and Neck Surgery,Beijing Children’s Hospital,CapitalMedical University,National Center for Children’s Health,Beijing,China [2]Department of Neurosurgery,Beijing Children’s Hospital,Capital Medical University,National Center for Children’s Health,Beijing,China [3]Department of Emergency Surgery,Beijing Children’s Hospital,Capital Medical University,National Center for Children’s Health,Beijing,China [4]Department of Pathology,Beijing Children’s Hospital,Capital Medical University,National Center for Children’s Health,Beijing,China

出　　处：《Pediatric Investigation》2022年第1期50-54,共5页儿科学研究（英文）

摘　　要：Introduction:Rosai-Dorfman disease(RDD)is an uncommon,benign,and idiopathic histiocytic proliferative disorder.Multiple intracranial RDD is extremely rare and treatment varies.Case presentation:A 9-year-old girl was admitted with 3-month history of blurred vision and facial paralysis,a 2-month history of recurrent giggle,and cognitive impairment.Computed tomography and magnetic resonance imaging scans revealed bilateral ventricular masses based on the dural membrane and the diameters of the masses were 9.1 cm and 9.2 cm,respectively.The lesions were completely removed with staging surgeries.Fifteen months after operation,blurred vision was still present but facial paralysis and giggle and cognitive impairment disappeared.Imaging examinations suggested that there were no new or recurring lesions.Conclusion:For multiple large intracranial masses,surgical treatment is necessary and staged surgery benefits perioperative safety.Active follow-up with magnetic resonance imaging is necessary.

关 键 词：INTRAVENTRICULAR PEDIATRIC Rosai-Dorfman disease Sinus histiocytosis Staging surgery 

分 类 号：R726.5[医药卫生—儿科]