儿童先天性鳃裂畸形的CT特征性表现  

Study on CT features of congenital branchial cleft anomaly in children

作　　者：周宜龙 陈伟[2] 徐蓉 陈佳瑞[2] 李晓艳[2] ZHOU Yilong;CHEN Wei;XU Rong;CHEN Jiarui;LI Xiaoyan(Department of Children Otorhinolaryngology,Shenzhen Hospital,Southern Medical University,Shenzhen,518000,China;Department of Otolaryngology Head and Neck Surgery,Shanghai Children’s Hospital,School of Medicine,Shanghai Jiao tong University;Department of Radiology and Medicine Imaging,Shanghai Children’s Hospital,School of Medicine,Shanghai Jiao tong University)

机构地区：[1]南方医科大学深圳医院儿童耳鼻咽喉科,广东深圳518100 [2]上海市儿童医院上海市交通大学医学院附属儿童医院耳鼻咽喉头颈外科 [3]上海市儿童医院上海市交通大学医学院附属儿童医院影像科

出　　处：《临床耳鼻咽喉头颈外科杂志》2022年第6期441-447,共7页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

基　　金：上海申康医院发展中心市级医院临床研究培育项目(No:SHDC12019X21)。

摘　　要：目的:总结儿童先天性鳃裂畸形CT特征性表现,以减少误诊和指导制定手术方案。方法:回顾性分析上海市儿童医院2014年8月-2021年1月收入院并经手术和病理确诊的先天性第1鳃裂畸形(CFBCA)、先天性第2鳃裂畸形(CSBCAs)、先天性梨状窝瘘(CPSF)的患儿CT影像学资料。结果:共收集儿童先天性鳃裂畸形323例,其中CFBCA 119例(119/323,36.8%),96例(96/119,80.67%)与外耳道壁相关,89例(89/119,74.78%)与腮腺相关,CT检查阳性率87.4%(104/119);CSBCAs57例(57/323,17.6%),其中46例(46/57,80.7%)与下颌下腺相关,CT检查阳性率84.2%(48/57);CPSF147例(147/323,45.5%),其中129例(129/147,87.8%)与甲状腺相关,CT检查阳性率89.1%(131/147)。结论:CFBCA的CT特征性表现为病灶位于同侧外耳道(底、后)壁及腮腺,CSBCAs的CT特征性表现为病灶位于同侧下颌下腺(后、内)侧,CPSF的CT特征性表现为病灶位于甲状腺侧叶上极背侧。Objective:Abstract Objective:To summarize the CT features of congenital branchial cleft anomaly in children,to reduce misdiagnosis and improve surgical strategy.Methods:This study enrolled 323 pediatric patients with congenital first branchial cleft anomaly,congenital second branchial cleft anomaly and congenital piriform sinus fistula confirmed by surgery and post-operative histopathology,who was admitted to Shanghai Children’s hospital from August 2014 to January 2021.,CT imaging data were retrospectively analyzed.Results:A total of 323 children with congenital branchial cleft deformity were included.There were 145 males and 178 females,aged from 22 days to 15 years.119(119/323,36.8%)cases were diagnosed as congenital first branchial cleft anomaly.Among them,96 cases(96/119,80.67%)were related to the wall of external auditory canal,and 89 cases(89/119,74.78%)were related to parotid gland.The positive rate of CT examination was 87.4%(104/119).57 cases(57/323,17.6%)had congenital second branchial cleft anomaly.Among them,46 cases(46/57,80.7%)were related to submandibular gland.The positive rate of CT examination was 84.2%(48/57).147 cases(147/323,45.5%)had congenital piriform sinus fistula,in which 129 cases(129/147,87.8%)were related to thyroid.The positive rate of CT was 89.1%(131/147).Conclusion:The CT findings of congenital first branchial cleft anomaly are characterized by lesions in the inferior and/or posterior wall of ipsilateral external auditory canal and parotid gland.The CT features of congenital second branchial cleft anomaly are that the lesion is located on the ipsilateral submandibular gland(posterior and medial).The CT features of congenital piriform sinus fistula are that the focus is located on the dorsal side of the upper pole of the lateral lobe of the thyroid gland.

关 键 词：儿童 先天性鳃裂畸形 体层摄影术 X线计算机 

分 类 号：R445.3[医药卫生—影像医学与核医学]