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作 者:刘明坤[1] 章国伟 吴典明[1] 林志雄 郑伟军 方一凡[1] LIU Mingkun;ZHANG Guowei;WU Dianming;LIN Zhixiong;ZHENG Weijun;FANG Yifan(Department of Pediatric Surgery,Fujian Maternity and Child Health Hospital College of Clinical Medicine for Obstetrics&Gynecology and Pediatrics,Fujian Medical University,Fuzhou 350001,China;Department of Radiology,Fujian Maternity and Child Health Hospital College of Clinical Medicine for Obstetrics&Gynecology and Pediatrics,Fujian Medical University,Fuzhou 350001,China)
机构地区:[1]福建省妇幼保健院,福建医科大学妇儿临床医学院小儿外科,福州350001 [2]福建省妇幼保健院,福建医科大学妇儿临床医学院放射影像科,福州350001
出 处:《福建医科大学学报》2022年第3期267-270,共4页Journal of Fujian Medical University
基 金:福建省科技创新联合资金项目(2020Y9139);福建医科大学启航基金项目(2019QH1141)。
摘 要:目的分析新生儿先天性细小结肠症的影像表现,以助于诊断原发疾病。方法收集2013年7月—2021年7月就诊并经结肠造影检查诊断为新生儿细小结肠的患儿325例,回顾性分析患儿的临床资料。结果325例中,男童175例,女童150例;平均出生胎龄(37.5±1.9)周(30~42+2周),其中足月儿290例,早产儿35例;就诊年龄0.5 h~14 d;正常出生体质量儿207例,低出生体质量儿118例。患儿均行腹部平片检查和结肠造影,最终确诊为单纯性先天性肠闭锁245例(75.4%)、肠闭锁合并胎粪性腹膜炎22例(6.8%)、肠闭锁合并先天性肠旋转不良10例(3.1%)、单纯胎粪性肠梗阻4例(1.2%)、先天性全结肠巨结肠31例(9.5%)、先天性巨结肠同源病10例(3.1%)、巨膀胱细小结肠肠蠕动不良综合征3例(0.9%)。结论新生儿细小结肠症病例依据腹部X射线检查、结肠造影特征表现以及临床表现可初步进行病因分析,为临床决策提供参考依据。Objective To analyze the imaging manifestations of congenital parvocolitis in neonates for the diagnosis of the primary disease. Methods A retrospective analysis was performed on the data of congenital microcolon in neonates diagnosed by colography from July 2013to July 2021. Results A total of 325cases were collected,including 175 males and 150females. Average gestational age at birth(37.5±1.9)weeks. There were more term infants(290cases)than premature infants(35cases). The age of treatment was 0.5hto 14d. There were more normal birth weight infants(207cases)than low birth weight infants(118cases). Among 325cases of congenital microcolon,the most cases(245cases,75.4%)were diagnosed as simple congenital intestinal atresia;22cases(6.8%)of Intestinal atresia combined with meconium peritonitis;10cases(3.1%)of intestinal atresia combined with congenital malrotation;4cases(1.2%)of simple meconium ileus;31cases(9.5%)of congenital Hirschsprung's disease.10cases(3.1%)of Hirschsprung's disease allied disorders;3cases(0.9%)of macrocystis parvoxel colonic dysmotility syndrome. Conclusion According to the abdominal X-ray,colography and clinical symptoms,congenital microcolon can be preliminarily. It can provide the basis for clinical decision making.
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