儿童罕见食管错构瘤的诊疗方法  

Diagnosis and treatment of rare esophageal hamartoma in children

作　　者：张谦[1] 曾骐 张娜[1] 陈诚豪 于洁[1] 严冬 徐长琪 刘鼎义 张旭[1] Zhang Qian;Zeng Qi;Zhang Na;Chen Chenghao;Yu Jie;Yan Dong;Xu Changqi;Liu Dingyi;Zhang Xu(Department of Thoracic Surgery,Beijing Children's Hospital,Capital Medical University,National Center for Children’s Health,Key Laboratory of Major Diseases in Children,Ministry of Education,Beijing 100045,China)

机构地区：[1]国家儿童医学中心,儿科重大疾病研究教育部重点实验室,首都医科大学附属北京儿童医院胸外科,北京100045

出　　处：《中华胸心血管外科杂志》2022年第7期409-412,共4页Chinese Journal of Thoracic and Cardiovascular Surgery

摘　　要：目的总结儿童食管错构瘤的临床特征及诊疗经验。方法回顾性分析我院2013年12月至2019年12月收治的3例食管错构瘤的临床资料。结果3例患儿男1例,女2例,平均年龄6.4岁。临床表现为呕吐2例,吞咽困难伴食管异物感1例。食管造影、胸部增强CT和食管镜可见食管狭窄或食管占位,病变段以上食管扩张。术中见肿瘤位于食管上段1例,食管下段2例。3例均完整切除肿瘤,术后顺利出院。3例随访10~74个月,平均37个月,复查造影存在胃食管反流1例。所有患儿复查CT或造影均未见狭窄和复发,目前均能正常饮食。结论儿童食管错构瘤以呕吐和喘憋为主要表现,术前诊断较困难,手术完整切除是主要治疗方法,预后良好。Objective To summarize the clinical features,diagnosis and treatment experience of esophageal hamartoma in children.Methods From December 2013 to December 2019,3 cases of esophageal hamartoma were admitted to our hospital,and a retrospective analysis was conducted.Results There were 1 male and 2 females,with an average age of 6.4 years old.The clinical manifestations were vomiting in 2 cases and dysphagia with esophageal foreign body sensation in 1 case.Esophagography,chest contrast-enhanced CT,and esophagoscopy showed esophageal stenosis or esophageal mass effectg,and esophageal dilatation above the affected segment.The tumor was found in upper esophagus in 1 case and lower esophagus in 2 cases.Tumors were complete resection in all 3 cases and the patients were discharged smoothly.All the 3 cases were followed up after surgery for 10-74 months(average 37 months),and 1 case had gastroesophageal reflux.No stenosis or recurrence was found in all the cases,and all the patients could eat normal diet.Conclusion The main manifestations of esophageal hamartoma in children are vomiting and choking.Complete surgical resection is the main treatment method,and the prognosis is good.

关 键 词：食管肿瘤 错构瘤 食管狭窄 

分 类 号：R735.1[医药卫生—肿瘤]