腹内型韧带样纤维瘤病的临床特征与声像图分析  

Clinical and Sonographic Features of Intra-abdominal Desmoid-type Fibromatosis

作　　者：韩洁 王勇 胡志广[2] 杨娣 王博 刘孟嘉 李宇辰 Han Jie;Wang Yong;Hu Zhiguang;Yang Di;Wang Bo;Liu Mengjia;Li Yuchen(National Cancer Center/National Clinical Research Center for Cancer/Cancer Hospital,Chinese Academy of Medical Sciences and Peking Union Medical College,Beijing 100021,China;National Cancer Center/National Clinical Research Center for Cancer/Hebei Cancer Hospital,Chinese Academy of Medical Sciences,Langfang,Hebei06500l,China)

机构地区：[1]国家癌症中心/国家肿瘤临床医学研究中心/中国医学科学院北京协和医学院肿瘤医院超声科,北京市100021 [2]国家癌症中心/国家肿瘤临床医学研究中心/河北中国医学科学院肿瘤医院超声科,河北省廊坊市065001

出　　处：《中国超声医学杂志》2022年第10期1132-1134,共3页Chinese Journal of Ultrasound in Medicine

基　　金：国家自然科学基金面上项目(No.81974268);东城区优秀人才培养资助项目;中国癌症基金会北京希望马拉松专项基金(No.LC2020B02)。

摘　　要：目的 探讨腹内型韧带样纤维瘤病(IADF)的临床与声像图特征。方法 回顾性分析30例经病理证实的IADF的临床资料及其中16例的超声声像图特征。结果 30例患者中,男性16例,女性14例,平均年龄46岁。14例患者有腹部手术史。9例女性患者有孕产史,1例首发于孕晚期。除1例家族性腺瘤性息肉病(FAP)相关韧带样纤维瘤病(DF)为多发病灶外,余29例均为单发。16例行超声检查的病灶最大径2.7~11.0 cm,平均(7.0±2.6)cm,均呈膨胀性生长,多表现为形态规则、边界清晰、乏血供的不均匀低回声实性包块,其中2例可见“肠系膜吞噬征”。4例行超声造影(CEUS)检查的病灶均呈“快进慢退”的高增强。结论 结合患者的临床特征及声像图表现,对IADF的诊断具有重要的提示意义,但最终还需病理学确诊。Objective To investigate the clinical and sonographic features of intra-abdominal desmoid-type fibromatosis(IADF). Methods The clinical features of 30 IADF confirmed by histopathology and immunohistochemistry, and the sonographic characteristics of 16 cases were retrospectively reviewed. Results There were 16 males and 14 females, with mean age 46 years. 14 patients had a history of abdominal surgery. Nine females had a childbearing history, and one case was found in the third trimester initially. 29 cases had single lesion, except one familial adenomatosis polyposis(FAP)-related desmoid-type fibromatosis(DF) was multiple. On ultrasound images, the largest diameter of the masses was 2.7~11.0 cm [mean(7.0±2.6) cm]. All lesions were expansive growth, most of the lesions showed regular shape, clear boundary, poor blood supply, and heterogenous hypoechoic solid mass. Two cases showed “mesenteric engulfed sign”. Four IADF showed “fast in and slow out” hyperenhancement on contrast-enhanced ultrasound(CEUS).Conclusions The clinical and sonograhic features of IADF are valuable, but the final diagnosis depends on pathological efamination.

关 键 词：韧带样纤维瘤病 腹内型 临床特征 声像图 

分 类 号：R445.1[医药卫生—影像医学与核医学] R738.6[医药卫生—诊断学]