眼皮肤白化病合并双眼白内障1例并文献复习  

A case of oculocutaneous albinism combined with bilateral complicated cataract and literature review

作　　者：任晴 张枫[1] REN Qing;ZHANG Feng(Department of Ophthalmology,Binzhou People's Hospital,Shandong First Medical University,Binzhou 256610,Shandong,China)

机构地区：[1]山东第一医科大学附属滨州市人民医院眼科,山东滨州256610

出　　处：《山东大学耳鼻喉眼学报》2022年第6期66-69,共4页Journal of Otolaryngology and Ophthalmology of Shandong University

摘　　要：目的 报道1例白内障超声乳化联合人工晶状体(IOL)一期植入术在眼皮肤白化病(OCA)合并双眼白内障患者中的应用。方法 1例因双眼视力渐进性下降半年,患有OCA的66岁男性患者就诊眼科,经全身查体、视力、眼压、裂隙灯检查、眼科B超等眼科辅助检查及胸部CT平扫,诊断为双眼并发性白内障,先后行双眼白内障超声乳化联合IOL一期植入术治疗。术中左眼应用吲哚菁绿辅助囊膜染色。结果 术后双眼视力均提高,IOL位正,白内障术中及术后1个月随访均未出现并发症,患者满意术后效果。结论 应用白内障超声乳化联合IOL一期植入术治疗OCA并发性白内障有效,可提高视力、改善生活质量。诊治过程中,OCA患者的心理负担也应得到高度重视。Objective This study aimed to report a case of phacoemulsification and one-stage intraocular lens(IOL)implantation in a patient with oculocutaneous albinism(OCA),complicated with bilateral cataracts. Methods A66-year-old male patient with OCA presented with a half-year history of progressive decline of binocular vision. After a general physical examination,visual acuity testing,intraocular pressure testing,slit lamp examination,ophthalmic B-ultrasound,other ophthalmic auxiliary examinations,and a chest computed tomography scan,the patient was diagnosed with bilateral complicated cataracts. He underwent bilateral cataract phacoemulsification and IOL implantation. His left eye was stained with an indocyanine green-assisted capsule. Results The patient’s visual acuity improved after postoperative. The position of the IOL was correct,and no postoperative complication was observed in his1-month follow-up. The patient was satisfied with the postoperative results. Conclusion The application of cataract phacoemulsification,combined with a one-stage IOL implantation,is effective in treating OCA-complicated cataracts,improving the patients’ vision and quality of life. The psychological burden of OCA patients should also be considered in their diagnosis and treatment.

关 键 词：眼皮肤白化病 并发性白内障 晶状体超声乳化 人工晶状体 眼球震颤 虹膜透照缺损 

分 类 号：R776.1[医药卫生—眼科] R751[医药卫生—临床医学]