幼儿Dandy-Walker综合征外科处理所带来的思考及文献总结  

Surgical management of Dandy-Walker syndrome in infants and the literature review

作　　者：王晓强[1] 李继如 王蕴坤 夏昊[2] 邢莉莉[2] 王位苹 Wang Xiaoqiang;Li Jiru;Wang Yunkun;Xia Hao;Xing Lili;Wang Weiping(Department of Pediatric Neurosurgery,Xinhua Hospital Affiliated to Shanghai Jiaotong University School of Medicine,Shanghai 200092,China;Department of Pediatric Critical Care Medicine,Xinhua Hospital Affiliated to Shanghai Jiaotong University School of Medicine,Shanghai 200092,China)

机构地区：[1]上海交通大学医学院附属新华医院小儿神经外科,上海200092 [2]上海交通大学医学院附属新华医院小儿急危重症医学科,上海200092

出　　处：《中国综合临床》2023年第2期118-121,共4页Clinical Medicine of China

摘　　要：Dandy-Walker综合征是后颅窝畸形之一,容易与蛛网膜囊肿或者小脑发育不良混淆,导致误诊。Dandy-Walker综合征容易合并脑积水,引起颅内压增高、头围增大、生长发育迟缓、痉挛性偏瘫等表现,还可以伴发神经系统其他畸形。于2021年2月27日上海交通大学医学院附属新华医院收治1例以生长发育迟缓为为首要表现的Dandy-Walker综合征患儿,经过多次手术治疗,患儿脑积水明显好转。通过对该患儿手术、并发症治疗等临床资料分析,有助于提高临床医生对该疾病外科治疗的认识。Dandy-Walker syndrome is one of the posterior fossa malformations,which is easily confused with arachnoid cyst or cerebellar dysplasia in clinical practice,leading to misdiagnosis.Dandy-Walker syndrome is easy to be combined with hydrocephalus,resulting in increased intracranial pressure,increased head circumference,growth retardation,spastic hemiplegia and other manifestations,and can also be accompanied by other nervous system malformations.On February 27,2021,a child with Dandy-Walker syndrome with growth retardation as the primary manifestation was admitted to Xinhua Hospital Affiliated to Shanghai Jiaotong University School of Medicine.After multiple surgical treatment,the child's hydrocephalus was significantly improved.Through the analysis of the clinical data of the child's operation and the treatment of complications,it is helpful to improve the clinicians'understanding of the surgical treatment of the disease.

关 键 词：DANDY-WALKER综合征 后颅窝囊肿 脑积水 囊肿切除术 脑室腹腔分流术 

分 类 号：R726.5[医药卫生—儿科]