中国儿童血管炎诊断与治疗系列专家共识之三——白塞综合征  

Consensus on diagnosis and treatment of childhood vasculitis in China:Behcet’s syndrome

作　　者：中国医师协会儿科医师分会风湿免疫学组 陈风华 唐雪梅 安云飞 孙良忠 胡坚[4] Academic Groupof Pediatric Rheumatology and Immunology,Society of Pediatrics of Chinese Medical Doctor Association;TANG Xue-mei;HU Jian

机构地区：[1]不详 [2]重庆医科大学附属儿童医院 [3]南方医科大学南方医院 [4]天津市儿童医院

出　　处：《中国实用儿科杂志》2023年第6期407-412,共6页Chinese Journal of Practical Pediatrics

摘　　要：白塞综合征是一种多系统变异性血管炎性疾病,主要累及口腔及生殖器黏膜、皮肤、消化道和眼部等。本病通常发生在青壮年,15%~20%于儿童时期起病。儿童白塞综合征在临床表现、疾病严重程度方面均与成人有所不同。由于缺乏特定的实验室指标,儿童从发病到出现典型临床表现之间往往有较长时间间隔,故儿童白塞综合征的诊断及治疗更具有挑战性。该共识依据国内外成人相关指南及儿童分类标准,结合国内部分风湿免疫专家意见形成,可为规范国内儿童白塞综合征的诊断与治疗提供参考依据。Behcet’s syndrome is a kind of inflammatory vessel disease with multi-system variable,which mainly involves oral and genital mucosa,skin,digestive tract and eyes.The disease usually occurs in young adults,with about 15%~20%of childhood onset.The clinical manifestation and severity of paediatric Behcet’s syndrome are different from those in adults.Due to the lack of specific laboratory indicators,there is often a long time interval between the onset of Behcet’s syndrome and the emergence of typical clinical manifestations,so the diagnosis and treatment of paediatric Behcet’s syndrome are more challenging.Based on adult guidelines and child classification standards and combined with the opinions of some domestic rheumatology and immunology experts,this consensus aims to provide a reference basis for standardizing the diagnosis and treatment of paediatric Behcet’s syndrome in China.

关 键 词：儿童白塞综合征 共识 诊断 治疗 

分 类 号：R72[医药卫生—儿科]