盆腔内炎性肌纤维母细胞瘤临床及MRI分析  

Clinical and MRI Analysis of Inflammatory Myofibroblastoma in Pelvic Cavity

作　　者：王晓艳[1] 张焱[1] 程敬亮[1] 胡瑛[1] 王岸飞[1] WANG Xiao-yan;ZHANG Yan;CHENG Jing-liang;HU Ying;WANG An-fei(Department of Magnetic Resonance Imaging,The First Affiliated Hospital of Zhengzhou University,Zhengzhou 450052,Henan Province,China)

机构地区：[1]郑州大学第一附属医院磁共振科,河南郑州450052

出　　处：《中国CT和MRI杂志》2023年第7期151-153,共3页Chinese Journal of CT and MRI

摘　　要：目的探讨盆腔内不同部位的炎性肌纤维母细胞瘤重要特征及预后。方法2012年7月至2022年8月经郑州大学第一附属医院病理证实盆腔内炎性肌纤维母细胞瘤患者10例,收集完整临床表现、病理及MRI资料。结果10例中,3例位于盆腔内软组织,4例位于子宫,1例位于前列腺,2例位于膀胱。表现为血尿、自触肿块、疼痛及发热。MRI表现为T1WI等信号,T2WI稍高信号,DWI高信号;增强后渐进性强化。ALK阳性率为40%。4例死亡,余6例术后未复发或转移。结论炎性肌纤维母细胞瘤是一种类似恶性肿瘤的中间型肿瘤,MRI检查能定位病变部位,明确范围及周围情况,确诊需结合免疫组织化学检查、组织病理学。但其有复发和远处转移潜能,术后需密切随访。Objective To investigate the important features and prognosis of inflammatory myofibroblastoma in different parts of pelvic cavity.Methods A total of 10 patients with pelvic inflammatory myofibroblastoma confirmed by pathology in the First Affiliated Hospital of Zhengzhou University from July 2012 to August 2022 were enrolled.The complete clinical manifestations,pathology and MRI data were collected.Results Of the 10 cases,3 cases were located in the pelvic soft tissue,4 cases in the uterus,1 case in the prostate and 2 cases in the bladder.The symptoms include hematuria,selftouching mass,pain and fever.MRI showed equal signal on T1WI,slightly high signal on T2WI,and high signal on DWI.Gradual enhancement after enhancement.The positive rate of ALK was 40%.4 patients died,and the remaining 6 patients had no recurrence or metastasis.Conclusion Inflammatory myofibroblastoma is an intermediate type of tumor similar to malignant tumor.MRI can locate the lesion site,clarify the scope and surrounding conditions.The diagnosis should be combined with immunohistochemistry and histopathology.However,it has the potential of recurrence and distant metastasis,and should be followed up closely after operation.

关 键 词：炎性肌纤维母细胞瘤 ALK 临床表现 病理 MRI 

分 类 号：R445.2[医药卫生—影像医学与核医学]