假性室间隔膜部瘤合并室间隔缺损的心脏CT影像学及临床特征分析  

Analysis of cardiac CT imaging and clinical characteristics of false aneurysm of the membranous septum with ventricular septal defect

作　　者：马彩彩 郑敏文 薛瑞佳 彭锐 赵宏亮 MA Caicai;ZHENG Minwen;XUE Ruijia;PENG Rui;ZHAO Hongliang(Department of Radiology,Xijing Hospital,Air Force Medical University,Xi'an 710032,China)

机构地区：[1]空军军医大学西京医院放射科,陕西西安710032

出　　处：《空军军医大学学报》2023年第8期726-728,733,共4页Journal of Air Force Medical University

基　　金：陕西省重点研发计划项目(S2020-YF-YBSF-0576)。

摘　　要：目的分析假性室间隔膜部瘤(FAMS)合并室间隔缺损(VSD)患者心脏CT血管造影(CTA)影像学及临床特征。方法回顾性分析空军军医大学西京医院2010年1月至2022年1月临床确诊的73例FAMS合并VSD患者心脏CTA影像资料,记录膜部瘤心脏CTA影像特征、合并心血管畸形及并发症。结果73例FAMS患者中,以菜花型最多(58.9%,43/73),且常常合并2处以上VSD;其次漏斗型(26.0%,19/73);囊袋型(12.3%,9/73)、弯管型(2.7%,2/73)最少。17例(23.3%,17/73)FAMS患者合并心血管畸形,常见的心血管畸形为主动脉缩窄(6.8%,5/73)和房间隔缺损(5.5%,4/73)。继发性心脏改变主要是右心房增大和三尖瓣反流,其中囊袋型FAMS患者发生率高于菜花型和漏斗型(P<0.05)。结论FAMS合并VSD患者,以菜花型多见,菜花型FAMS易合并多个VSD。FAMS患者主要合并主动脉缩窄、房间隔缺损等心血管畸形。继发性心脏改变主要为右心房增大及三尖瓣中大量反流,尤其以囊袋型发生率最高。Objective To analyze the cardiac CT angiography(CTA)imaging and clinical characteristics in patients with false aneurysm of the membranous septum(FAMS)with ventricular septal defect(VSD).Methods The cardiac CTA imaging data of 73 patients with FAMS combined with VSD diagnosed in Xijing Hospital,Air Force Medical University from January 2010 to January 2022 were retrospectively analyzed,and the cardiac CTA imaging characteristics of FAMS,combined cardiovascular malformations and complications were recorded.Results Among the 73 patients with FAMS,cauliflower type was the most common(58.9%,43/73),and often combined with more than 2 VSDs,followed by funnel type(26.0%,19/73),sack type(12.3%,9/73),and siphon type(2.7%,2/73).Seventeen patients(23.3%,17/73)with FAMS were combined with cardiovascular malformations.The common cardiovascular malformations were coarctation of the aorta(6.8%,5/73)and atrial septal defect(5.5%,4/73).The secondary cardiac changes were mainly right atrial enlargement and tricuspid regurgitation,which were more common in patients with sack type FAMS than in the other three types(P<0.05).Conclusion Cauliflower type is the most common type in patients with FAMS combined with VSD.Cauliflower type FAMS is often combined with multiple VSDs.FAMS patients are mainly complicated with cardiovascular malformations such as coarctation of the aorta and atrial septal defect.The secondary cardiac changes were mainly right atrial enlargement and medium to massive tricuspid regurgitation,especially in patients with sack type FAMS.

关 键 词：室间隔膜部瘤 室间隔缺损 心脏CT造影 

分 类 号：R541[医药卫生—心血管疾病]