多脾综合征的MSCT影像学表现及鉴别诊断  

MSCT imaging manifestations and differential diagnosis of polysplenia syndrome

作　　者：王冰 谢宝君[1] 杨文兵[1] 查云飞[1] WANG Bing;XIE Baojun;YANG Wenbing;ZHA Yunfei(Dept.of Radiology,Renmin Hospital of Wuhan University,Wuhan 430060,Hubei,China)

机构地区：[1]武汉大学人民医院放射科,湖北武汉430060

出　　处：《武汉大学学报（医学版）》2023年第8期1006-1010,1017,共6页Medical Journal of Wuhan University

摘　　要：目的:分析总结多脾综合征患者的多层螺旋CT(MSCT)影像学表现及诊断价值,提高对其认识及准确诊断。方法:回顾性分析2013年1月至2021年6月于武汉大学人民医院确诊的13例多脾综合征患者的临床资料和MSCT影像资料。结果:总结了13例多脾综合征患者MSCT的影像学表现。(1)多个脾结节:数目不等,4~21个;脾结节位置位于右腹部9例,左腹部4例。(2)内脏异常:全内脏反位者7例;短胰者7例,中位水平肝脏、中位胆囊者4例。(3)心血管畸形:心脏异常者2例,均为复杂型先心病;下腔静脉肝内段缺如者4例,奇静脉扩张并与上腔静脉异常连接者4例。(4)双肺畸形:双肺左侧肺形态者2例。(5)伴发肿瘤:伴发胃间质瘤1例,直肠癌2例。结论:多脾综合征是一种以多系统先天性联合畸形为特征的综合征,其影像学表现多样,胸腹部CT检查有助于其全面诊断,可减少临床误诊漏诊的发生。Objective:To analyze and summarize the multi⁃slice computed tomography(MSCT)imaging manifestations and diagnostic values of polysplenia syndrome,for improving the awareness and accu⁃rate diagnosis of polysplenia syndrome.Methods::The clinical and MSCT imaging data of 13 patients confirmed polysplenia syndrome were analyzed retrospectively.Results::All the 13 cases had multiple spleen nodes,and the numbers of spleen nodes ranged from 4 to 21.Nine cases were located in the right abdomen,and the other 4 in the left.Of these 13 cases,full situs inversus was found in 7 cases,short pancreas in 7 cases,and midline live and midline gallbladder in 4 cases.The cardiac anomalies were seen in 2 cases.Inferior vena cava hepatic segment absent and the azygos vein dilation connec⁃tion with the superior vena cava were present in 4 cases.The symmetrical left lung was seen in 2 cas⁃es,and 1 case of gastric stromal tumor and 2 cases of rectal cancer were found.Conclusion::Polysple⁃nia syndrome is a disorder characterized by a combination of multiple congenital malformations.Un⁃derstanding the various CT imaging findings could increase awareness of the polysplenia syndrome and reduce the clinical misdiagnosis and missed diagnosis.

关 键 词：多脾综合征 MSCT 脾结节 内脏反位 心血管畸形 

分 类 号：R445.3[医药卫生—影像医学与核医学]