儿童特发性肺含铁血黄素沉着症的诊治进展  

Progress in Diagnosis and Treatment of Idiopathic Pulmonary Hemosiderosis in Children

作　　者：魏梦月 李惠民[2] 刘素琴 WEI Mengyue;LI Huimin;LIU Suqin(Department of Pediatrics,Yangzhou Women and Children Care Service Hospital Affiliated to Yangzhou University,Yangzhou 225002,China;DepartmentⅡof Respiration,Beijing Children's Hospital Affiliated to Capital Medical University,Beijing 100045,China)

机构地区：[1]扬州大学附属医院扬州市妇幼保健院儿科,扬州225002 [2]首都医科大学附属北京儿童医院呼吸二科,北京100045

出　　处：《药学与临床研究》2023年第4期347-351,共5页Pharmaceutical and Clinical Research

摘　　要：特发性肺含铁血黄素沉着症(IPH),主要特征是反复出现的弥漫性肺泡出血,临床表现以反复发作的小细胞低色素性贫血以及咳嗽、咯血等呼吸道症状为主。该病的诊断主要为排除性诊断,目前治疗以肾上腺皮质激素为主,辅以类固醇助减剂及免疫抑制剂,本文将对近年来的诊断及治疗研究进展进行综述。Idiopathic pulmonary hemosiderosis(IPH)is mainly characterized by repeated diffuse alveolar hemorrhage.Common clinical manifestations include recurrent small cell hypochromic anemia and respiratory symptoms such as cough,hemoptysis.The diagnosis of this disease is mainly through exclusion.Currently,the main treatment is adrenocortical hormone,supplemented with steroid-sparing agent and immunosuppressants.This paper will review the research progress of diagnosis and treatment in recent years.

关 键 词：特发性肺含铁血黄素沉着症 儿童 诊断 治疗 

分 类 号：R725[医药卫生—儿科]