儿童烟雾病的磁共振诊断价值  

The diagnostic value of MRI in detecting pediatric moyamoya disease

作　　者：郭桂芳 杨礼 白敏[1] GUO Guifang;YANG Li;BAI Min(Department of Radiology,People's Hospital of Liaocheng City,Liaocheng 252000,China;Department of Radiology,Maternal and Child Health Care Hospital of Liaocheng District of Dongchangfu City,Liaocheng 252004,China)

机构地区：[1]山东省聊城市人民医院影像科,山东聊城252000 [2]山东省聊城市东昌府区妇幼保健院放射科,山东聊城252004

出　　处：《医学影像学杂志》2023年第8期1343-1346,共4页Journal of Medical Imaging

摘　　要：目的探讨儿童烟雾病(moyamoya disease,MMD)的临床和磁共振表现特征。方法选取28例有临床症状且同时行MRI检查并确诊为MMD患儿进行回顾性分析。所有患儿均行MRI常规扫描(包括T_(1)WI、T_(2)WI、T_(2)-FLAIR)、DWI及3D TOF MRA检查,7例行3D ASL检查。结果28例患儿男性11例,女性17例,年龄2~12岁。患儿主要临床表现为抽搐(15例)、肢体无力(9例)、头痛(5例)等。MRA表现为颈内动脉末端、大脑前、中动脉近端不同程度的狭窄或闭塞,累及双侧者26例,单侧者2例,颅底均可见异常血管网形成。MRI表现为脑梗死16例,脑缺血4例,脑出血2例,仅表现为常春藤征2例,脑萎缩1例,脑MRI正常3例。7例行3D ASL检查,3例脑内存在灌注减低区。结论儿童MMD有特征性的影像学表现,MRI常规扫描结合DWI及3D TOF MRA、3D ASL可全面评价儿童MMD,指导临床早期诊断治疗。Objective To evaluate the clinical and magnetic resonance features of Moyamoya disease(MMD)in children.Methods Retrospective analysis was performed on 28 children with clinical symptoms who were diagnosed with MMD by MRI examination.All children received conventional MRI scan(including T_(1)WI,T_(2)WI and T_(2)-FLAIR),DWI and 3D TOF MRA examinations,and 7 children received 3D ASL examination.Results There were 17 females and 11 males,aged from 2 years to 12 years.The symptoms included convulsion(15 cases),limb weakness(9 cases),headache(5 cases),etc.MRA showed different degrees of stenosis or occlusion at the terminal end of internal carotid artery,proximal end of anterior and middle cerebral artery,involving 26 bilateral cases,2 unilateral cases.The abnormal vascular network in the skull was observed.The MRI showed cerebral infarction in 16 cases,cerebral ischemia in 4 cases,cerebral hemorrhage in 2 cases,only Ivy sign in 2 cases,brain atrophy in 1 case,and normal brain MRI in 3 cases.Seven patients underwent 3D ASL examination,and 3 patients had decreased cerebral perfusion area.Conclusion There are characteristic imaging manifestations of pediatric moyamoya disease.Conventional MRI combined with DWI,3D TOF MRA and 3D ASL can comprehensively evaluate pediatric moyamoya disease and guide early clinical diagnosis and treatment.

关 键 词：儿童 烟雾病 磁共振成像 磁共振血管成像 动脉自旋标记 

分 类 号：R725.9[医药卫生—儿科] R445.2[医药卫生—临床医学]