Poland综合征的临床特征和治疗研究进展  

Progress in clinical manifestations and treatment of Poland syndrome

作　　者：喻月 岑瑛[1] YU Yue;CEN Ying(Department of Plastic and Burn Surgery,West China Hospital,Sichuan University,Chengdu,Sichuan 610041,P.R.China)

机构地区：[1]四川大学华西医院整形外科/烧伤科,成都610041

出　　处：《华西医学》2023年第9期1417-1422,共6页West China Medical Journal

摘　　要：Poland综合征是一种以单侧胸壁发育不良或缺失,同时伴有不同程度同侧肢体缺陷为典型特征的先天性畸形。由于目前Poland综合征的病因尚未明确,且没有统一规范的临床分类及诊疗方案,临床容易误诊、漏诊,从而延误治疗时机并且影响治疗效果。通过查阅近年来国内外Poland综合征诊疗的相关文献,该文从病因、临床表现及分型、诊断及治疗几个方面进行总结阐述,以期提升对Poland综合征的认知,为规范临床诊疗提供参考,提高诊治效率。Poland syndrome is a congenital anomaly characterized by unilateral underdeveloped or absent chest wall,accompanied by varying degrees of ipsilateral limb defects.In clinical practice,Poland syndrome is prone to misdiagnosis and missed diagnosis,which delays treatment timing and affects treatment effectiveness,as the current etiology is not yet clear and there is no unified and standardized clinical classification and treatment plan.This article summarizes and elaborates on the etiology,clinical manifestations,classification,diagnosis,and treatment of Poland syndrome by reviewing relevant literature on the diagnosis and treatment of Poland syndrome both domestically and internationally in recent years,in order to enhance understanding of Poland syndrome,provide reference for standardized clinical diagnosis and treatment,and improve the efficiency of diagnosis and treatment.

关 键 词：POLAND综合征 胸廓畸形 并指 分类标准 临床治疗 

分 类 号：R725.9[医药卫生—儿科]