脊髓受累原发性中枢神经系统血管炎的临床研究进展  

Recent advance in primary central nervous system vasculitis with spinal cord involvement

作　　者：张莉[1,2] 孙慧[1] 张世敏 高赛[1] 武雷[1] 黄德晖[1] Zhang Li;Sun Hui;Zhang Shimin;Gao Sai;Wu Lei;Huang Dehui(Faculty of Medicine,Department of Neurology,First Medical Center of PLA General Hospital,Beijing 100853,China;Department of Neurology,First People's Hospital of Nanyang City)

机构地区：[1]解放军总医院第一医学中心神经内科医学部,北京100853 [2]河南省南阳市第一人民医院神经内科

出　　处：《中华神经医学杂志》2023年第9期960-964,共5页Chinese Journal of Neuromedicine

摘　　要：原发性中枢神经系统血管炎(PACNS)是一种罕见的中枢神经系统免疫性疾病,脊髓受累是其罕见亚型。该亚型影像学表现缺乏特异性,易误诊、漏诊,疾病的复发率、致残性及致死率亦较高。本文现围绕脊髓受累PACNS患者的临床表现、诊断及治疗方式做一综述,以期增加临床医生对该病的认识。Primary angiitis of the central nervous system(PACNS)is a rare autoimmune disease of the central nervous system,and spinal cord involvement is a rare subtype.The imaging findings of this subtype lack specificity;it is easily misdiagnosed,missed diagnosed,enjoying high disease recurrence rate,disability and mortality.Therefore,this article reviews the clinical manifestations,diagnoses and treatments of PACNS patients with spinal cord involvement,in order to increase clinicians'understanding of the disease.

关 键 词：原发性中枢神经系统性血管炎 脊髓病变 磁共振成像 电生理检查 

分 类 号：R593.2[医药卫生—内科学] R747.9[医药卫生—临床医学]