Ⅰ型神经纤维瘤病性胸腰椎脊柱侧后凸的围术期临床疗效及护理研究  

The Clinical Outcomes and Perioperative Care of Neurofibromatosis Type 1 Thoracolumbar Kyphoscoliosis

作　　者：杨莹 田雪 陈亚萍 赵钇伟 李子全 YANG Ying;TIAN Xue;CHEN Yaping;ZHAO Yiwei;LI Ziquan(Department of Orthopaedic Surgery,Beijing Key Laboratory for Genetic Research of Skeletal Deformity,Key Laboratory of Big Data for Spinal Deformities,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100730,China)

机构地区：[1]中国医学科学院北京协和医院骨科,骨骼畸形遗传学研究北京市重点实验室,中国医学科学院脊柱畸形大数据研究与应用重点实验室,北京100730

出　　处：《罕见病研究》2023年第4期539-546,共8页Journal of Rare Diseases

摘　　要：目的评估后路矫形融合术治疗Ⅰ型神经纤维瘤病(NF1)性胸腰椎脊柱侧后凸的围术期疗效及并发症,并探索此类患者的护理模式。方法回顾性分析我科于2012年3月至2022年4月收治的134例NF1性胸腰椎脊柱侧后凸患者,统计分析手术疗效与围术期并发症,对患者进行围术期全程护理评估,探索此类患者的围术期护理模式,针对性开展NF1性胸腰椎脊柱侧后凸患者的观察要点及评估指标。结果NF1性胸腰椎脊柱侧后凸患者术前营养状态、肺功能相对较差,手术时间、出血量、截骨矫形等级相对较高;出现术后并发症概率高。本组患者均顺利完成手术,脊柱侧凸矫正率为(528±227)%,脊柱后凸矫形率为(573±346)%,25例患者发生并发症,未出现神经损伤等严重围术期并发症。结论针对性NF1性胸腰椎脊柱侧后凸患者的围术期护理模式有助于加速患者恢复,预防或及时发现并发症,提高治疗效果。Objective To evaluate the clinical outcomes and complications of posterior spinal fusion surgery in the treatment of neurofibromatosis type 1(NF1)thoracolumbar kyphoscoliosis,and to explore the mode of perioperative care for nurses provided to the patients.Methods We used the retrospective analysis on the 134 patients with NF1 thoracolumbar kyphoscoliosis admitted to our department from March 2012 to April 2022 and analyzed the clinical outcomes and perioperative complications by using the related statistics.We eval-uated the Perioperative care by the nurses in the treatment of NF1 to explore the mode of nursing to the patients with the NF1,by using specific observation points and evaluation indicators.Results NF1 kyphoscoliosis pa-tients had poor preoperative nutritional status and lung function.NF1 kyphoscoliosis underwent longer operation time,lost more blood in operation,had higher osteotomy grade and more postoperative complications.All the patients successfully completed the operation in our group.The correction rate of scoliosis was(528±227)%,and the correction rate of kyphosis was(573±346)%.25 patients had complications but no such serious complications as nerve damage.Conclusions The practice of the perioperative nursing to NF1 type scoliosis patients facilitates the shortening of the recovery period,the prevention or timely detection of complications,and improvement of the therapeutic effect.

关 键 词：Ⅰ型神经纤维瘤病性脊柱侧后凸 临床护理 并发症 矫形效果 

分 类 号：R473[医药卫生—护理学] R682.3[医药卫生—临床医学]