新生儿门体分流2例报道并文献复习  

Congenital portosystemic shunts:2 cases report and review of literature

作　　者：徐嘉欣 戴立英 张健[1] 王娟[2] 刘瑜[2] XU Jiaxin;DAI Liying;ZHANG Jian;WANG Juan;LIU Yu(Department of Neonatology,Anhui Medical University/Anhui Children's Hospital,Hefei,Anhui 230000,China;不详)

机构地区：[1]安徽医科大学附属省儿童医院/安徽医科大学第五临床医学院新生儿科,安徽合肥230000 [2]安徽医科大学附属省儿童医院新生儿科,安徽合肥230000

出　　处：《中华全科医学》2023年第12期2173-2176,共4页Chinese Journal of General Practice

基　　金：中央医疗服务与保障能力提升项目(Z155080000004);安徽省卫生健康科研项目(AHWJ2022b087)。

摘　　要：增加临床医生对先天性门体分流(CPSS)的认识,重视患儿病史细节,达到尽早发现、制定个性化治疗方案的目的。回顾分析近10年在安徽省儿童医院就诊并治疗的2例新生儿CPSS临床资料,并以“先天性门体分流”“先天性门静脉分流”“新生儿”“Congenital portosystemic shunts”“Abernethy syndrome”“Infants”“Case report”为关键词检索2010年1月1日—2022年12月31日发表在中国知网、万方数据库、维普网数据库、PubMed、GeenMedical、Web of Science的中英文文献,通过去重、删除资料不全文献,共纳入相关文献10篇,共118例患者,进行文献复习。分析其临床表现、相关合并症、治疗及预后,以增强临床医师对先天性门静脉分流的认识,提高对该病的诊断和管理能力。To increase clinicians'awareness of congenital portosystemic shunts,pay attention to the details of the child's medical history,achieve early detection and develop individualized treatment plans.Retrospective analysis of clinical data of 2 cases of CPSS in children seen and treated at Anhui Children's Hospital in the past 10 years.Then we systematically searched relevant studies in Chinese and English literature between January 1,2010 and December 31,2022 in databases of China Knowledge Network,Wanfang database,Vipshop database,PubMed,GeenMedical,Web of Science using congenital portosystemic shunts,Abernethy syndrome,infants,case report as the keywords.After removing the duplicates and those with incomplete data,we conducted a review of 10 studies with 118 cases.Our analysis of the clinical manifestations,diagnosis and treatment of these cases may help to improve clinicians'understanding of congenital portosystemic shunts and their ability to diagnose and manage the condition.

关 键 词：先天性门体分流 新生儿 ABERNETHY畸形 自发闭合 文献复习 

分 类 号：R722.1[医药卫生—儿科]