Biventricular isolated apical hypoplasia:First-time description of a new cardiac abnormality by multimodality imaging  

作　　者：Fabio Chirillo Michee Fusaro Giovanni Baestriero Chiara Aderighi Umberto Cucchini 

机构地区：[1]Department of Cardiology,Ospedale san Bassiano,Bassano del Grappa(Ⅵ),Italy 2Department of Radiology,Ca’Foncello Hospital,Treviso,Italy

出　　处：《Discussion of Clinical Cases》2022年第4期1-6,共6页临床病例讨论杂志（英文版）

摘　　要：Left ventricular isolated hypoplasia is a seldom-described cardiac abnormality.Right ventricular hypoplasia is usually associated with congenital anomalies of the pulmonary or the tricuspid valve,whereas biventricular isolated apical hypoplasia has never been described.We report the case of a 48-year-old man with no history of known cardiac disease who was found to have a complex cardiac abnormality characterized by:1)Deficiency of the myocardium within the biventricular apex with adipose tissue infiltration;2)Truncated right ventricle because of an absent trabecular portion of the inflow tract;3)Truncated and spherical left ventricular apex;4)Origin of the mitral papillary muscle in the flattened anterior left ventricular apex.Multimodality imaging was performed to delineate the morphological and functional characteristics of this cardiomyopathy fully.To the best of our knowledge,this is the first description of a new cardiac abnormality characterized by the hypoplasia of the apical region of both ventricles in the absence of valvular or coronary artery disease.

关 键 词：Isolated apical hypoplasia BIVENTRICULAR Echocardiography Computed tomography Cardiac magnetic resonance imaging 

分 类 号：R541[医药卫生—心血管疾病]