左室心肌致密化不全研究进展  

Research Progress of Left Ventricular Noncompaction

作　　者：管勤朝 和倩 朱高沣 肖榆冰 高云光 GUAN Qinzhao;HE Qian;ZHU Gaofeng;XIAO Yubing;GAO Yunguang(The First Affiliated Hospital of Dali University,Dali 671000,China;不详)

机构地区：[1]大理大学第一附属医院功能科,云南大理671000 [2]大理大学第一附属医院感染科,云南大理671000 [3]大理大学第一附属医院儿科,云南大理671000

出　　处：《中国医学创新》2024年第1期174-178,共5页Medical Innovation of China

摘　　要：左室心肌致密化不全(left ventricular noncompaction,LVNC)是一种以心室壁内粗大肌小梁和深陷小梁隐窝为特征的罕见遗传性心肌病,具体病因及发病机制尚不明确。本文主要对LVNC的流行病学、病因、发病机制、临床表现、诊疗及预后进行综述,以期更好指导LVNC的临床诊疗。Left ventricular noncompaction is a rare hereditary cardiomyopathy characterized by thick trabeculae and deep recessed trabeculae in the ventricular wall.The etiology and pathogenesis of LVNC remains unclear.This article reviews the epidemiology,etiology,pathogenesis,clinical manifestations,diagnosis,treatment and prognosis of LVNC with a view to better guiding the clinical diagnosis and treatment of LVNC.

关 键 词：左室心肌致密化不全 心肌病 诊断 治疗 

分 类 号：R542.2[医药卫生—心血管疾病]