全内脏反位肝移植的研究进展  

Research progress in liver transplantation in patients with situs inversus totalis

作　　者：王安琪 汤睿[2] 卢倩 Wang Anqi;Tang Rui;Lu Qian(Graduate School of Qinghai University,Department of Hepatopancreatobiliary Surgery,the Affiliated Hospital of Qinghai University,Xining 810001,China;不详)

机构地区：[1]青海大学研究生院青海大学附属医院肝胆胰外科,西宁810001 [2]清华大学临床医学院清华大学附属北京清华长庚医院肝胆胰中心

出　　处：《器官移植》2024年第2期270-275,共6页Organ Transplantation

基　　金：国家自然科学基金(92168207);中国医学科学院医学与健康科技创新工程创新单元(2019-I2M-5-056)。

摘　　要：全内脏反位(SIT)是一种非常罕见的先天性疾病,在人群中发病率极低,不患病的SIT人群与普通人没有差别。但是当此类人群患病时,由于缺少对此类人群的认识,导致在对SIT人群进行诊断及治疗非常困难,尤其是SIT人群合并终末期肝病需要进行肝移植手术时,无论是SIT人群作为肝移植的供者或受者,对于外科医师而言都是巨大的挑战。本文通过查阅国内外近些年发表的SIT肝移植相关个案报道,对SIT肝移植在国内外的发展历程,SIT肝移植的关键步骤、预后及术后并发症等进行综述。Situs inversus totalis(SIT) is a rare congenital condition,with an extremely low incidence.There is no difference between SIT individuals without onset of diseases and healthy counterparts.However,when SIT individuals suffer from diseases,the diagnosis and treatment are highly challenging due to insufficient understanding of SIT populations,especially for those complicated with end-stage liver disease and requiring liver transplantation.It is a huge challenge for surgeons whether SIT individuals serve as donors or recipients of liver transplantation.In this article,recent case reports related to liver transplantation in SIT patients were summarized,and the development,key procedures,clinical prognosis and postoperative complications of liver transplantation in SIT patients were reviewed.

关 键 词：全内脏反位 肝脏解剖 先天性疾病 肝移植 供肝摆放 脉管吻合 术后并发症 Roux-en-Y胆肠吻合 

分 类 号：R617[医药卫生—外科学]