头颈部Rosai-Dorfman病的影像学表现(5例报道并文献分析)  

Imaging Findings of Rosai-Dorfman Disease in the Head and Neck(Report 5 Cases and Analysis of the Literature)

作　　者：区婉仪 胡茂清 朱新进[1,2] OU Wanyi;HU Maoqing;ZHU Xinjin(Guangdong Medical University,Zhanjiang,Guangdong Province 524000,P.R.China)

机构地区：[1]广东医科大学,湛江524000 [2]佛山市第二人民医院影像中心,528000 [3]江门市中心医院放射科,529030

出　　处：《临床放射学杂志》2024年第2期309-313,共5页Journal of Clinical Radiology

摘　　要：目的探讨头颈部Rosai-Dorfman病(RDD)的影像学表现,以提高对该病的认识。方法回顾性分析经手术病理证实的头颈部5例RDD患者的临床和影像资料,结合文献总结其影像学特征。2例患者进行了CT检查,3例患者同时进行了CT和MRI检查。结果淋巴结型2例,表现为双侧颈部、颌下多发淋巴结增大,部分融合,密度均匀,病灶轻-中度均匀强化;混合型2例表现为鼻腔鼻窦内不规则肿块,鼻道狭窄,肿块明显强化,上颌骨部分破坏伴明显强化,同时见颈部淋巴结增大;结外型1例表现为左侧额顶部脑膜结节状增厚,明显强化,可见脑膜尾征。结论头颈部RDD的影像表现有一定的特异性,需结合病理才能做出准确诊断。Objective To explore the imaging findings of Rosai-Dorfman's disease(RDD)in the head and neck in order to improve the diagnosis of the disease.Methods The clinical and imaging data of 5 patients with RDD confirmed by pathology were analyzed retrospectively,and their imaging features were summarized in combination with the literature.CT was performed in 2 cases,CT and MRI were performed in 3 cases.Results Lymph node type was found in 2 cases,which showed bilateral cervical and submandibular lymph node enlargement,partial fusion,homogeneous density,and mild to moderate homogeneous enhancement of the lesions.Two mixed cases showed irregular masses in the nasal cavity and sinuses,narrowing of the nasal passages,marked enhancement of the masses,partial destruction of the maxillae with obvious enhancement,and cervical lymph node enlargement.One case of extranodal type showed nodular thickening of the left parietal meninges with marked enhancement and meningeal tail sign.Conclusion The imaging manifestation of Rosai-Dorfman disease in the head and neck has certain specificity,which needs to be combined with pathological findingsto make an accurate diagnosis.

关 键 词：头颈部 ROSAI-DORFMAN病 体层摄影术 X线计算机 磁共振成像 

分 类 号：R551.2[医药卫生—血液循环系统疾病] R445[医药卫生—内科学]