Fontan循环的新时代——远期淋巴系统并发症研究进展  

New Era of Fontan Circulation—Research Progress in Long-Term Lymphatic System Complications

作　　者：杜楚豪 董捷 董硕 刘顺 徐海涛[1] 孙阳雪 李守军[1] 杨克明[1] 闫军[1] DU Chuhao;DONG Jie;DONG Shuo;LIU Shun;XU Haitao;SUN Yangxue;LI Shoujun;YANG Keming;YAN Jun(Department of Pediatric Cardiac Surgery,Fuwai Hospital,National Center for Cardiovascular Diseases,Chinese Academy of Medical Sciences and Peking Union Medical College,Beijing 100037,China)

机构地区：[1]中国医学科学院,北京协和医学院,国家心血管病中心,阜外医院小儿外科中心,北京100037

出　　处：《心血管病学进展》2024年第4期299-302,共4页Advances in Cardiovascular Diseases

基　　金：中国医学科学院临床与转化医学研究基金(2020-I2M-C&T-B-060)。

摘　　要：全腔静脉-肺动脉连接术(Fontan姑息手术)挽救了大量单心室结构患儿的生命。然而,术后远期淋巴系统并发症严重影响着患者的预后。现回顾既往相关文献,总结Fontan术后患者淋巴系统并发症的自然病程、病理生理、临床表现、诊断和治疗管理。Total cavopulmonary connection(Fontan procedure)has saved the lives of a large number of children with single ventricle,in which a biventricular repair is not possible.However,postoperative long-term lymphatic system complications seriously affect the prognosis of patients.This article reviews the previous literature and summarizes the natural history,pathophysiology,clinical manifestations,diagnosis,and management of lymphatic system complications in patients with Fontan circulation.

关 键 词：Fontan循环 淋巴系统并发症 塑型性支气管炎 蛋白丢失性肠病 淋巴管介入治疗 

分 类 号：R726.5[医药卫生—儿科]