先天性感音神经性耳聋患儿内耳道狭窄与蜗神经管异常的HRCT表现  

HRCT features of internal auditory canal stenosis and abnormality of cochlear nerve canal in children with congenital sensorineural hearing loss

作　　者：孙积宁[1] 于海燕 王文娟[1] 张保隆[2] SUN Jining;YU Haiyan;WANG Wenjuan;ZHANG Baolong(Department of Radiology,Weifang People’s Hospital,Weifang 261011,China;Department of Radiology,Weifang Maternal and Child Health Hospital,Weifang 261011,China)

机构地区：[1]山东省潍坊市人民医院放射科,山东潍坊261011 [2]山东省潍坊市妇幼保健院放射科,山东潍坊261011

出　　处：《中国中西医结合影像学杂志》2024年第5期523-525,553,共4页Chinese Imaging Journal of Integrated Traditional and Western Medicine

基　　金：山东省医药卫生科技发展计划项目(202009010058)。

摘　　要：目的:探讨先天性感音神经性耳聋(SNHL)患儿内耳道狭窄与蜗神经管异常的HRCT表现及2种畸形的相关性。方法:回顾性分析67例(75耳)存在先天性SNHL,且HRCT诊断为内耳道狭窄和/或蜗神经管异常患儿的CT资料。结果:67例(75耳)均有蜗神经管异常,双侧8例、单侧59例(左耳30例、右耳29例);其中30耳合并内耳道狭窄,16耳合并其他内耳结构畸形。28例(30耳)内耳道狭窄中,双侧2例、单侧26例(左耳11例、右耳15例),8耳合并半规管、前庭或耳蜗畸形。内耳道狭窄与蜗神经管异常均以单侧发病为主,左右耳均可发病,差异均无统计学意义(均P>0.05)。结论:SNHL患儿中蜗神经管异常比内耳道狭窄更常见,也更具临床意义,但易漏诊,应引起高度重视,建议行内耳HRCT检查常规测量蜗神经管宽度。Objective:To explore the HRCT features of internal auditory canal(IAC)stenosis and abnormality of cochlear nerve canal(CNC)in children with congenital sensorineural hearing loss(SNHL)and the correlation between IAC stenosis and CNC abnormality.Methods:The images of 67 children with congenital SNHL were analyzed retrospectively,all children had IAC stenosis and/or CNC abnormality diagnosed by HRCT.Results:67 cases(75 ears)had CNC abnormality,8 cases were with bilateral abnormalities and 59 cases with unilateral abnormalities(30 left ears,29 right ears),and among the 75 ears,30 ears complicated with IAC stenosis and 16 ears with other internal ear abnormality.Of the 28 cases(30 ears)with IAC stenosis,2 cases were bilateral stenosis and 26 cases unilateral(11 left ears,15 right ears),8 ears complicated with abnormality of semicircular canal,vestibule or cochlea.IAC stenosis and CNC abnormality were mainly unilateral,and both left and right ears could develop,with no statistically significant differences(both P>0.05).Conclusions:In SNHL children,CNC abnormality is more common than IAC stenosis and has more clinical significance.However,CNC abnormality is easy to be misdiagnosed,which should be highly valued.It is suggested that the CNC width should be routinely measured in the internal ear HRCT.

关 键 词：内耳道 蜗神经管 畸形 体层摄影术 X线计算机 

分 类 号：R764.431[医药卫生—耳鼻咽喉科] R816.96[医药卫生—临床医学]