声门下区Rosai-Dorfman病1例并文献复习  

Infraglottic portion Rosai-Dorfman disease:a case report

作　　者：胡成浩 高冯翔 张英[1] 郭斌[1] HU Chenhao;GAO Fengxiang;ZHANG Ying;GUO Bin(Department of Otolaryngology,Qinghai University Affiliated Hospital,Xining,810001,China)

机构地区：[1]青海大学附属医院耳鼻咽喉科,青海西宁810001

出　　处：《临床耳鼻咽喉头颈外科杂志》2024年第8期755-757,共3页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

摘　　要：Rosai-Dorfman病是一种罕见的非朗格汉斯组织细胞疾病,具有淋巴结内和(或)结外表现。目前尚无治疗这种疾病的指导方案。本文报道1例声门下区的病例,患者未表现出典型的症状,如发烧或淋巴结病,术前极易被误诊为恶性肿瘤。患者接受了低温等离子微创手术联合激素治疗,获得良好疗效。本文通过对Rosai-Dorfman病相关文献进行回顾,以便更好地了解此种罕见疾病的临床表现、诊断和治疗。Rosai Dorfman disease is a rare non Langerhans histiocytic disease with intranodal and/or extranodal manifestations,most commonly affecting cervical lymph nodes.There is no treatment guideline for this disease.This paper reports a case of infraglottic portion,which did not show typical symptoms,such as fever or lymphadenopathy,and was easily misdiagnosed as malignant tumor preoperatively.The patient underwent low-temperature plasma minimally invasive surgery combined with hormone therapy and achieved good clinical effect.By reviewing the literature,we can better understand the clinical manifestations,diagnosis and treatment of this rare disease.

关 键 词：Rosai-Dorfman disease 声门下疾病 外科手术 

分 类 号：R767.44[医药卫生—耳鼻咽喉科]