Unroofed coronary sinus,left-sided superior vena cava and mitral insufficiency:A case report and review of the literature  

作　　者：Fouad Bitar Ziad Bulbul Yehya Jassar Rana Zareef Jennifer Abboud Mariam Arabi Fadi Fouad Bitar 

机构地区：[1]Department of Pediatric and Adolescent,American University of Beirut Medical Center,Beirut 1103,Lebanon [2]Department of Surgery,American University of Beirut Medical Center,Beirut 1103,Lebanon

出　　处：《World Journal of Cardiology》2024年第10期595-603,共9页世界心脏病学杂志（英文）

摘　　要：BACKGROUND Unroofed coronary sinus(UCS)is a rare subtype of atrial septal defect.It is frequently associated with a persistent left superior vena cava and is often part of a more intricate cardiac malformation.CASE SUMMARY This report describes a rare case of an adolescent patient with UCS featuring atrial situs solitus,absence of the right superior vena cava and a persistent left superior vena cava draining into the left atrium consistent with total unroofing of the coronary sinus.This was associated with concurrent severe mitral insufficiency secondary to redundant and prolapsing leaflets,and a substantial left-to-right shunt across the coronary sinus orifice.A comprehensive examination of the existing literature is included,shedding light on the diagnostic challenges of UCS and describing the available surgical options within the context of mitral valve surgery.CONCLUSION UCS is a complex condition requiring careful consideration of associated anomalies and a tailored surgical approach.

关 键 词：Unroofed coronary sinus Mitral insufficiency Single left superior vena cava Surgical options Absent right superior vena cava Case report 

分 类 号：R654.2[医药卫生—外科学]