Therapeutic endoscopic retrograde cholangiopancreatography in a patient with asplenia-type heterotaxy syndrome:A case report  

作　　者：Yu-Yan Zhang Jiang Ruan Yan Fu 

机构地区：[1]Department of Gastroenterology,The Second Affiliated Hospital of Kunming Medical University,Kunming 650101,Yunnan Province,China

出　　处：《World Journal of Gastrointestinal Surgery》2024年第11期3578-3583,共6页世界胃肠外科杂志（英文）

摘　　要：BACKGROUND Asplenia-type heterotaxy syndrome(HS)is rare and refers to visceral malposition and dysmorphism.It is associated with a high infant mortality rate due to cardiac anomalies,and related digestive endoscopic interventions are poorly understood.With the improved long-term prognosis of these individuals after modern cardiac surgery,intra-abdominal anomalies have become increasingly significant.CASE SUMMARY Herein,we report successful endoscopic retrograde cholangiopancreatography(ERCP)in a 14-year-old male with asplenia-type HS that involved unique imaging findings and technical difficulties.His anatomic anomalies included complex congenital heart disease,midline liver placement,an absent spleen,a left-sided inferior vena cava,and dextroposition of the stomach and pancreas.He suffered from choledocholithiasis with obstructive jaundice,and the stone was successfully extracted with a basket following endoscopic papillary balloon dilation.CONCLUSION Although anatomic anomalies in HS increase the degree of technical difficulty when performing ERCP,they can be safely managed by experienced endosco-pists,as illustrated by the present case.Identifying these variations with imaging modalities and being aware of them before initiating an invasive intervention are crucial to preventing potential complications.

关 键 词：HETEROTAXY ASPLENIA Situs ambiguous Endoscopic retrograde cholangiopan-creatography Case report 

分 类 号：R657.4[医药卫生—外科学]