肝内胆管腺纤维瘤伴血管增生1例并文献复习  

Intrahepatic biliary adenofibroma with vascular proliferation:a case report and literature review

作　　者：万翠霞 陈湘光[1] WAN Cuixia;CHEN Xiangguang(Department of Radiology,Meizhou People’s Hospital,Meizhou 514031,China)

机构地区：[1]梅州市人民医院放射科,梅州514031

出　　处：《国际医学放射学杂志》2024年第6期739-742,共4页International Journal of Medical Radiology

摘　　要：目的 探讨肝内胆管腺纤维瘤(BAF)的CT和MRI特征,以提高对该肿瘤的认识。方法 回顾性分析1例经病理证实为BAF的CT和MRI表现并复习相关文献。结果 CT平扫可见肝右叶一团片状低密度影,边界欠清,其内可见斑点状钙化灶;增强扫描病灶边缘及内部分隔呈渐进性明显强化,部分呈类血管样强化,囊性成分未见强化。MRI可见肝右叶一团片状异常信号影,边界欠清,病灶内可见多发分隔、呈蜂窝状改变,T1WI呈稍低/低信号,T2WI呈稍高/高信号,扩散加权成像(DWI)呈稍高信号,表观扩散系数(ADC)值增高;增强扫描病灶边缘及分隔呈渐进性强化,肝胆期局部高信号。结论 BAF罕见,其影像表现具有一定的特征并可评估良恶性,确诊需病理及免疫组化检查。Objective Investigating the CT and MRI characteristics of intrahepatic biliary adenofibroma(BAF)to improve the understanding of this tumor.Methods We conducted a retrospective analysis of the CT and MRI findings from one case confirmed by pathology as BAF,alongside a review of relevant literature.Results The CT plain scan reveals a slightly hypodense mass in the right liver lobe,with poorly defined borders,and punctate calcifications within.On contrast-enhanced scans,the margins and internal septa of the lesion exhibited progressive marked enhancement,with some exhibiting vascular-like enhancement,while the cystic components show no enhancement.MRI demonstrated an abnormal signal mass in the right liver lobe,with unclear borders,multiple septa,and a honeycomb-like appearance.On T1-weighted imaging(T1WI),the mass showed slightly low to low signal intensity,while on T2-weighted imaging(T2WI),it displayed slightly high to high signal intensity.Diffusion-weighted imaging(DWI)indicated slightly high signal intensity,and the apparent diffusion coefficient(ADC)values were increased.On enhanced scans,the lesion’s margins and septa showed progressive enhancement,with localized high signals during the hepatic-biliary phase.Conclusion BAF is a rare entity with distinctive imaging features that may aid in differentiating between benign and malignant lesions.A definitive diagnosis,however,requires pathological and immunohistochemical examination.

关 键 词：肝脏 胆管腺纤维瘤 体层摄影术 X线计算机 磁共振成像 

分 类 号：R814.42[医药卫生—影像医学与核医学] R816.5[医药卫生—放射医学]